Categorias DeCS
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.398 Lipid Metabolism, Inborn Errors .
C16.320.565.398.465 Hyperlipoproteinemia Type I .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.584 Lipid Metabolism Disorders .
C18.452.584.500 Dyslipidemias .
C18.452.584.500.500 Hyperlipidemias .
C18.452.584.500.500.644 Hyperlipoproteinemias .
C18.452.584.500.500.644.237 Hyperlipoproteinemia Type I .
C18.452.584.500.875 Hypolipoproteinemias .
C18.452.584.500.875.440 Hypobetalipoproteinemias .
C18.452.584.500.875.440.750 Hypobetalipoproteinemia, Familial, Apolipoprotein B .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.398 Lipid Metabolism, Inborn Errors .
C18.452.648.398.465 Hyperlipoproteinemia Type I .
D10 Lipids .
D10.532 Lipoproteins .
D10.532.091 Apolipoproteins .
D10.532.091.300 Apolipoproteins B .
D12 Amino Acids, Peptides, and Proteins .
D12.776 Proteins .
D12.776.070 Apoproteins .
D12.776.070.400 Apolipoproteins .
D12.776.070.400.300 Apolipoproteins B .
D12.776.521 Lipoproteins .
D12.776.521.120 Apolipoproteins .
D12.776.521.120.300 Apolipoproteins B .
Termos Sinônimos e Históricos Documentos LILACS e MDL
Hyperlipoproteinemia Type I . Burger-Grutz Syndrome . C-II Anapolipoproteinemia . Chylomicronemia, Familial . Familial Fat-Induced Hypertriglyceridemia . Familial Hyperchylomicronemia . Familial Hyperlipoproteinemia Type 1 . Familial LPL Deficiency . Familial Lipoprotein Lipase Deficiency . Hyperlipemia, Essential Familial . Hyperlipemia, Idiopathic, Burger-Grutz Type . Hyperlipoproteinemia Type Ia . Hyperlipoproteinemia Type Ib . Hyperlipoproteinemia, Type I . Hyperlipoproteinemia, Type Ia . Hyperlipoproteinemia, Type Ib . LIPD Deficiency . Lipase D Deficiency . Lipoprotein Lipase Deficiency . Anapolipoproteinemia, C-II . Anapolipoproteinemias, C-II . Apolipoprotein C II Deficiency . Apolipoprotein C-II Deficiencies . Burger Grutz Syndrome . Burger-Grutz Syndromes . C-II Anapolipoproteinemias . Chylomicronemias, Familial . Deficiencies, Apolipoprotein C-II . Deficiencies, Familial LPL . Deficiencies, LIPD . Deficiencies, Lipase D . Deficiencies, Lipoprotein Lipase . Deficiency, Apolipoprotein C-II . Deficiency, Familial LPL . Deficiency, LIPD . Deficiency, Lipase D . Deficiency, Lipoprotein Lipase . Essential Familial Hyperlipemia . Essential Familial Hyperlipemias . Familial Chylomicronemia . Familial Chylomicronemias . Familial Fat Induced Hypertriglyceridemia . Familial Fat-Induced Hypertriglyceridemias . Familial Hyperchylomicronemias . Familial Hyperlipemia, Essential . Familial Hyperlipemias, Essential . Familial LPL Deficiencies . Fat-Induced Hypertriglyceridemia, Familial . Fat-Induced Hypertriglyceridemias, Familial . Hyperchylomicronemias, Familial . Hyperlipemias, Essential Familial . Hyperlipoproteinemia Type Ias . Hyperlipoproteinemia Type Ibs . Hyperlipoproteinemia Type Is . Hyperlipoproteinemias, Type I . Hyperlipoproteinemias, Type Ia . Hyperlipoproteinemias, Type Ib . Hypertriglyceridemia, Familial Fat-Induced . Hypertriglyceridemias, Familial Fat-Induced . LIPD Deficiencies . LPL Deficiencies, Familial . LPL Deficiency, Familial . Lipase D Deficiencies . Lipase Deficiencies, Lipoprotein . Lipoprotein Lipase Deficiencies . Syndrome, Burger-Grutz . Syndromes, Burger-Grutz . Type I Hyperlipoproteinemia . Type I Hyperlipoproteinemias . Type Ia Hyperlipoproteinemia . Type Ia Hyperlipoproteinemias . Type Ib Hyperlipoproteinemia . Type Ib Hyperlipoproteinemias . Apolipoprotein C-II Deficiency . Hyperchylomicronemia, Familial . Lipoprotein Lipase Deficiency, Familial . 0.74