Categorias DeCS
C10 Nervous System Diseases .
C10.228 Central Nervous System Diseases .
C10.228.140 Brain Diseases .
C10.228.140.163 Brain Diseases, Metabolic .
C10.228.140.163.100 Brain Diseases, Metabolic, Inborn .
C10.228.140.163.100.435 Lysosomal Storage Diseases, Nervous System .
C10.228.140.163.100.435.825 Sphingolipidoses .
C10.228.140.163.100.435.825.700 Niemann-Pick Diseases .
C10.228.140.163.100.435.825.700.500 Niemann-Pick Disease, Type A .
C15 Hemic and Lymphatic Diseases .
C15.604 Lymphatic Diseases .
C15.604.250 Histiocytosis .
C15.604.250.410 Histiocytosis, Non-Langerhans-Cell .
C15.604.250.410.625 Niemann-Pick Diseases .
C15.604.250.410.625.500 Niemann-Pick Disease, Type A .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.189 Brain Diseases, Metabolic, Inborn .
C16.320.565.189.435 Lysosomal Storage Diseases, Nervous System .
C16.320.565.189.435.825 Sphingolipidoses .
C16.320.565.189.435.825.700 Niemann-Pick Diseases .
C16.320.565.189.435.825.700.500 Niemann-Pick Disease, Type A .
C16.320.565.398 Lipid Metabolism, Inborn Errors .
C16.320.565.398.641 Lipidoses .
C16.320.565.398.641.803 Sphingolipidoses .
C16.320.565.398.641.803.730 Niemann-Pick Diseases .
C16.320.565.398.641.803.730.500 Niemann-Pick Disease, Type A .
C16.320.565.595 Lysosomal Storage Diseases .
C16.320.565.595.554 Lysosomal Storage Diseases, Nervous System .
C16.320.565.595.554.825 Sphingolipidoses .
C16.320.565.595.554.825.700 Niemann-Pick Diseases .
C16.320.565.595.554.825.700.500 Niemann-Pick Disease, Type A .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.132 Brain Diseases, Metabolic .
C18.452.132.100 Brain Diseases, Metabolic, Inborn .
C18.452.132.100.435 Lysosomal Storage Diseases, Nervous System .
C18.452.132.100.435.825 Sphingolipidoses .
C18.452.132.100.435.825.700 Niemann-Pick Diseases .
C18.452.132.100.435.825.700.500 Niemann-Pick Disease, Type A .
C18.452.584 Lipid Metabolism Disorders .
C18.452.584.687 Lipidoses .
C18.452.584.687.803 Sphingolipidoses .
C18.452.584.687.803.730 Niemann-Pick Diseases .
C18.452.584.687.803.730.500 Niemann-Pick Disease, Type A .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.189 Brain Diseases, Metabolic, Inborn .
C18.452.648.189.435 Lysosomal Storage Diseases, Nervous System .
C18.452.648.189.435.825 Sphingolipidoses .
C18.452.648.189.435.825.700 Niemann-Pick Diseases .
C18.452.648.189.435.825.700.500 Niemann-Pick Disease, Type A .
C18.452.648.398 Lipid Metabolism, Inborn Errors .
C18.452.648.398.641 Lipidoses .
C18.452.648.398.641.803 Sphingolipidoses .
C18.452.648.398.641.803.730 Niemann-Pick Diseases .
C18.452.648.398.641.803.730.500 Niemann-Pick Disease, Type A .
C18.452.648.595 Lysosomal Storage Diseases .
C18.452.648.595.554 Lysosomal Storage Diseases, Nervous System .
C18.452.648.595.554.825 Sphingolipidoses .
C18.452.648.595.554.825.700 Niemann-Pick Diseases .
C18.452.648.595.554.825.700.500 Niemann-Pick Disease, Type A .
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| | Termos Sinônimos e Históricos | Documentos LILACS e MDL | |
| Niemann-Pick Disease, Type A . Classical Niemann-Pick Disease . Neuronal Cholesterol Lipidosis . Niemann-Pick Disease, Acute Neuronopathic Form . Niemann-Pick Disease, Acute Neurovisceral Form . Niemann-Pick Disease, Neuronopathic Type . Niemann-Pick's Disease Type A . Ophthalmoplegia, Supraoptic Vertical . Sphingomyelin Cholesterol Lipidosis . Sphingomyelin Lipidosis . Sphingomyelinase Deficiency . Type A Niemann-Pick Disease . Cholesterol Lipidoses, Neuronal . Cholesterol Lipidoses, Sphingomyelin . Cholesterol Lipidosis, Neuronal . Cholesterol Lipidosis, Sphingomyelin . Classical Niemann Pick Disease . Deficiencies, Sphingomyelinase . Deficiency, Sphingomyelinase . Lipidoses, Neuronal Cholesterol . Lipidoses, Sphingomyelin . Lipidoses, Sphingomyelin Cholesterol . Lipidosis, Neuronal Cholesterol . Lipidosis, Sphingomyelin . Lipidosis, Sphingomyelin Cholesterol . Neuronal Cholesterol Lipidoses . Niemann Pick Disease, Acute Neuronopathic Form . Niemann Pick Disease, Acute Neurovisceral Form . Niemann Pick Disease, Neuronopathic Type . Niemann Pick Disease, Type A . Niemann Pick's Disease Type A . Niemann-Pick Disease, Classical . Ophthalmoplegias, Supraoptic Vertical . Sphingomyelin Cholesterol Lipidoses . Sphingomyelin Lipidoses . Sphingomyelinase Deficiencies . Sphingomyelinase Deficiency Diseases . Supraoptic Vertical Ophthalmoplegia . Supraoptic Vertical Ophthalmoplegias . Type A Niemann Pick Disease . Vertical Ophthalmoplegia, Supraoptic . Vertical Ophthalmoplegias, Supraoptic . Sphingomyelinase Deficiency Disease . Classical Niemann-Pick Disease . 1.00
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