Categorias DeCS
C10 Nervous System Diseases .
C10.228 Central Nervous System Diseases .
C10.228.140 Brain Diseases .
C10.228.140.163 Brain Diseases, Metabolic .
C10.228.140.163.100 Brain Diseases, Metabolic, Inborn .
C10.228.140.163.100.540 Menkes Kinky Hair Syndrome .
C10.597 Neurologic Manifestations .
C10.597.606 Neurobehavioral Manifestations .
C10.597.606.643 Intellectual Disability .
C10.597.606.643.455 Mental Retardation, X-Linked .
C10.597.606.643.455.687 Menkes Kinky Hair Syndrome .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.322 Genetic Diseases, X-Linked .
C16.320.322.500 Mental Retardation, X-Linked .
C16.320.322.500.687 Menkes Kinky Hair Syndrome .
C16.320.322.968 X-Linked Combined Immunodeficiency Diseases .
C16.320.400 Heredodegenerative Disorders, Nervous System .
C16.320.400.525 Mental Retardation, X-Linked .
C16.320.400.525.687 Menkes Kinky Hair Syndrome .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.189 Brain Diseases, Metabolic, Inborn .
C16.320.565.189.540 Menkes Kinky Hair Syndrome .
C16.320.565.618 Metal Metabolism, Inborn Errors .
C16.320.565.618.590 Menkes Kinky Hair Syndrome .
C16.614 Infant, Newborn, Diseases .
C16.614.815 Severe Combined Immunodeficiency .
C16.614.815.500 X-Linked Combined Immunodeficiency Diseases .
C17 Skin and Connective Tissue Diseases .
C17.800 Skin Diseases .
C17.800.329 Hair Diseases .
C17.800.329.968 Menkes Kinky Hair Syndrome .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.132 Brain Diseases, Metabolic .
C18.452.132.100 Brain Diseases, Metabolic, Inborn .
C18.452.132.100.540 Menkes Kinky Hair Syndrome .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.189 Brain Diseases, Metabolic, Inborn .
C18.452.648.189.540 Menkes Kinky Hair Syndrome .
C18.452.648.618 Metal Metabolism, Inborn Errors .
C18.452.648.618.590 Menkes Kinky Hair Syndrome .
C20 Immune System Diseases .
C20.673 Immunologic Deficiency Syndromes .
C20.673.815 Severe Combined Immunodeficiency .
C20.673.815.500 X-Linked Combined Immunodeficiency Diseases .
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| | Termos Sinônimos e Históricos | Documentos LILACS e MDL | |
| Menkes Kinky Hair Syndrome . Congenital Hypocupremia . Copper Transport Disease . Kinky Hair Disease . Menkea Syndrome . Menkes Disease . Menkes' Disease . Steely Hair Disease . X-Linked Copper Deficiency . Congenital Hypocupremias . Copper Deficiencies, X-Linked . Copper Deficiency, X-Linked . Copper Transport Diseases . Deficiencies, X-Linked Copper . Deficiency, X-Linked Copper . Disease, Copper Transport . Disease, Steely Hair . Diseases, Copper Transport . Diseases, Kinky Hair . Diseases, Menkes' . Diseases, Steely Hair . Hair Diseases, Kinky . Hair Diseases, Steely . Hypocupremias, Congenital . Kinky Hair Diseases . Menkea Syndromes . Menkes' Diseases . Steely Hair Diseases . Steely Hair Syndromes . Syndrome, Menkea . Syndrome, Steely Hair . Syndromes, Menkea . Syndromes, Steely Hair . Transport Disease, Copper . Transport Diseases, Copper . X Linked Copper Deficiency . X-Linked Copper Deficiencies . Menkes Syndrome . Steely Hair Syndrome . Kinky Hair Syndrome . Hypocupremia, Congenital . 1.00
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| X-Linked Combined Immunodeficiency Diseases . Combined Immunodeficiency, X-Linked . Immunodeficiency 4 . Immunodeficiency 6 . Immunodeficiency Diseases, X-Linked Combined . SCID, X-Linked . SCIDX . SCIDX1 . Severe Combined Immunodeficiency, X-Linked . Severe Combined Immunodeficiency, X-Linked, T Cell Negative, B Cell Positive, NK Cell Negative . Severe Combined Immunodeficiency, X-Linked, T Cell-Negative, B Cell-Positive, NK Cell-Negative . X-Linked Combined Immunodeficiency . X-Linked Immunodeficiency Disease . X-Linked Immunodeficiency Syndrome . X-Linked SCID . X-SCID . XSCID . Combined Immunodeficiency, X Linked . Immunodeficiency Disease, X-Linked . Immunodeficiency Diseases, X Linked Combined . Immunodeficiency Diseases, X-Linked . Immunodeficiency Syndrome, X-Linked . Immunodeficiency Syndromes, X-Linked . Immunodeficiency, X-Linked Combined . SCID, X Linked . SCIDs, X-Linked . Severe Combined Immunodeficiency, X Linked . Syndromes, X-Linked Immunodeficiency . X Linked Combined Immunodeficiency . X Linked Combined Immunodeficiency Diseases . X Linked Immunodeficiency Disease . X Linked Immunodeficiency Syndrome . X Linked SCID . X Linked Severe Combined Immunodeficiency . X-Linked Combined Immunodeficiencies . X-Linked Immunodeficiency Diseases . X-Linked Immunodeficiency Syndromes . X-Linked SCIDs . X-Linked Severe Combined Immunodeficiency . 0.60
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