Categorias DeCS
C06 Digestive System Diseases .
C06.689 Pancreatic Diseases .
C06.689.150 Congenital Hyperinsulinism .
C10 Nervous System Diseases .
C10.228 Central Nervous System Diseases .
C10.228.140 Brain Diseases .
C10.228.140.163 Brain Diseases, Metabolic .
C10.228.140.163.100 Brain Diseases, Metabolic, Inborn .
C10.228.140.163.100.380 Hyperlysinemias .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.100 Amino Acid Metabolism, Inborn Errors .
C16.320.565.100.544 Hyperlysinemias .
C16.320.565.189 Brain Diseases, Metabolic, Inborn .
C16.320.565.189.380 Hyperlysinemias .
C16.614 Infant, Newborn, Diseases .
C16.614.200 Congenital Hyperinsulinism .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.132 Brain Diseases, Metabolic .
C18.452.132.100 Brain Diseases, Metabolic, Inborn .
C18.452.132.100.380 Hyperlysinemias .
C18.452.394 Glucose Metabolism Disorders .
C18.452.394.968 Hyperinsulinism .
C18.452.394.968.250 Congenital Hyperinsulinism .
C18.452.394.984 Hypoglycemia .
C18.452.394.984.200 Congenital Hyperinsulinism .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.100 Amino Acid Metabolism, Inborn Errors .
C18.452.648.100.544 Hyperlysinemias .
C18.452.648.189 Brain Diseases, Metabolic, Inborn .
C18.452.648.189.380 Hyperlysinemias .
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| | Termos Sinônimos e Históricos | Documentos LILACS e MDL | |
| Congenital Hyperinsulinism . Familial Hyperinsulinemic Hypoglycemia 1 . Familial Hyperinsulinism . Hyperinsulinemia Hypoglycemia of Infancy . Hyperinsulinemic Hypoglycemia Due to Focal Adenomatous Hyperplasia . Hyperinsulinemic Hypoglycemia, Familial, 1 . Hyperinsulinemic Hypoglycemia, Familial, 2 . Hyperinsulinemic Hypoglycemia, Persistent . Hyperinsulinism, Congenital . Hyperinsulinism, Familial . Hyperinsulinism, Neonatal . Hypoglycemia, Hyperinsulinemic, of Infancy . Infancy Hyperinsulinemia Hypoglycemia . Neonatal Hyperinsulinism . PHHI Hypoglycemia . Persistent Hyperinsulinemic Hypoglycemia . Congenital Hyperinsulinisms . Familial Hyperinsulinisms . Hyperinsulinemic Hypoglycemias, Persistent . Hyperinsulinisms, Congenital . Hyperinsulinisms, Familial . Hyperinsulinisms, Neonatal . Hypoglycemia, PHHI . Hypoglycemia, Persistent Hyperinsulinemic . Hypoglycemias, PHHI . Hypoglycemias, Persistent Hyperinsulinemic . Infancy Hyperinsulinemia Hypoglycemias . Neonatal Hyperinsulinisms . PHHI Hypoglycemias . Persistent Hyperinsulinemic Hypoglycemias . Persistent Hyperinsulinemia Hypoglycemia of Infancy . 1.00
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| Hyperlysinemias . Deficiency Disease, Alpha-Aminoadipic Semialdehyde . Deficiency Disease, Lysine Alpha-Ketoglutarate Reductase . Deficiency Disease, Saccharopine Dehydrogenase . Familial Hyperlysinemia . Hyperlysinemia . Hyperlysinemia, Familial . Hyperlysinemia, Periodic . Hyperlysinuria With Hyperammonemia . L-Lysine:NAD-Oxido-Reductase Deficiency . Lysine:Alpha-Ketoglutarate Reductase Deficiency . Alpha Aminoadipic Semialdehyde Deficiency Disease . Deficiencies, L-Lysine:NAD-Oxido-Reductase . Deficiencies, Lysine:Alpha-Ketoglutarate Reductase . Deficiency Disease, Alpha Aminoadipic Semialdehyde . Deficiency Disease, Lysine Alpha Ketoglutarate Reductase . Deficiency, L-Lysine:NAD-Oxido-Reductase . Deficiency, Lysine:Alpha-Ketoglutarate Reductase . Familial Hyperlysinemias . Hyperammonemia, Hyperlysinuria With . Hyperammonemias, Hyperlysinuria With . Hyperlysinemias, Familial . Hyperlysinemias, Periodic . Hyperlysinuria With Hyperammonemias . L Lysine:NAD Oxido Reductase Deficiency . L-Lysine:NAD-Oxido-Reductase Deficiencies . Lysine Alpha Ketoglutarate Reductase Deficiency Disease . Lysine:Alpha Ketoglutarate Reductase Deficiency . Lysine:Alpha-Ketoglutarate Reductase Deficiencies . Periodic Hyperlysinemia . Periodic Hyperlysinemias . Reductase Deficiencies, Lysine:Alpha-Ketoglutarate . Reductase Deficiency, Lysine:Alpha-Ketoglutarate . With Hyperammonemia, Hyperlysinuria . With Hyperammonemias, Hyperlysinuria . Alpha-Aminoadipic Semialdehyde Deficiency Disease . Lysine Alpha-Ketoglutarate Reductase Deficiency Disease . Saccharopine Dehydrogenase Deficiency Disease . 0.63
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