Categorias DeCS
C04 Neoplasms .
C04.445 Hamartoma .
C04.445.435 Hamartoma Syndrome, Multiple .
C04.445.435.500 Proteus Syndrome .
C04.651 Neoplasms, Multiple Primary .
C04.651.435 Hamartoma Syndrome, Multiple .
C04.651.435.500 Proteus Syndrome .
C05 Musculoskeletal Diseases .
C05.116 Bone Diseases .
C05.116.099 Bone Diseases, Developmental .
C05.116.099.370 Dysostoses .
C05.116.099.370.894 Synostosis .
C05.116.099.370.894.232 Craniosynostoses .
C05.116.099.370.894.232.015 Acrocephalosyndactylia .
C05.116.099.370.894.819 Syndactyly .
C05.116.099.370.894.819.100 Acrocephalosyndactylia .
C05.116.099.370.894.819.756 Poland Syndrome .
C05.116.099.750 Proteus Syndrome .
C05.660 Musculoskeletal Abnormalities .
C05.660.207 Craniofacial Abnormalities .
C05.660.207.240 Craniosynostoses .
C05.660.207.240.100 Acrocephalosyndactylia .
C05.660.585 Limb Deformities, Congenital .
C05.660.585.620 Proteus Syndrome .
C05.660.585.800 Syndactyly .
C05.660.585.800.100 Acrocephalosyndactylia .
C05.660.585.800.756 Poland Syndrome .
C05.660.906 Synostosis .
C05.660.906.364 Craniosynostoses .
C05.660.906.364.100 Acrocephalosyndactylia .
C05.660.906.819 Syndactyly .
C05.660.906.819.100 Acrocephalosyndactylia .
C05.660.906.819.756 Poland Syndrome .
C10 Nervous System Diseases .
C10.597 Neurologic Manifestations .
C10.597.606 Neurobehavioral Manifestations .
C10.597.606.643 Intellectual Disability .
C10.597.606.643.835 Trisomy 13 Syndrome .
C14 Cardiovascular Diseases .
C14.240 Cardiovascular Abnormalities .
C14.240.400 Heart Defects, Congenital .
C14.240.400.970 Trisomy 13 Syndrome .
C14.280 Heart Diseases .
C14.280.400 Heart Defects, Congenital .
C14.280.400.970 Trisomy 13 Syndrome .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.131 Congenital Abnormalities .
C16.131.077 Abnormalities, Multiple .
C16.131.077.740 Proteus Syndrome .
C16.131.077.919 Trisomy 13 Syndrome .
C16.131.077.944 Wolf-Hirschhorn Syndrome .
C16.131.240 Cardiovascular Abnormalities .
C16.131.240.400 Heart Defects, Congenital .
C16.131.240.400.965 Trisomy 13 Syndrome .
C16.131.260 Chromosome Disorders .
C16.131.260.923 Trisomy 13 Syndrome .
C16.131.260.985 Wolf-Hirschhorn Syndrome .
C16.131.621 Musculoskeletal Abnormalities .
C16.131.621.207 Craniofacial Abnormalities .
C16.131.621.207.240 Craniosynostoses .
C16.131.621.207.240.100 Acrocephalosyndactylia .
C16.131.621.585 Limb Deformities, Congenital .
C16.131.621.585.620 Proteus Syndrome .
C16.131.621.585.800 Syndactyly .
C16.131.621.585.800.100 Acrocephalosyndactylia .
C16.131.621.585.800.756 Poland Syndrome .
C16.131.621.906 Synostosis .
C16.131.621.906.364 Craniosynostoses .
C16.131.621.906.364.100 Acrocephalosyndactylia .
C16.131.621.906.819 Syndactyly .
C16.131.621.906.819.100 Acrocephalosyndactylia .
C16.131.621.906.819.756 Poland Syndrome .
C16.320 Genetic Diseases, Inborn .
C16.320.180 Chromosome Disorders .
C16.320.180.923 Trisomy 13 Syndrome .
C16.320.180.985 Wolf-Hirschhorn Syndrome .
C23 Pathological Conditions, Signs and Symptoms .
C23.550 Pathologic Processes .
C23.550.288 Disease .
C23.550.288.500 Syndrome .
C23.888 Signs and Symptoms .
C23.888.672 Prodromal Symptoms .
E01 Diagnosis .
E01.599 Prodromal Symptoms .
Termos Sinônimos e Históricos Documentos LILACS e MDL
Acrocephalosyndactylia . Acrocephalosyndactyly (Apert) . Acrocephalosyndactyly III . Acrocephalosyndactyly, Type 1 . Acrocephalosyndactyly, Type 3 . Acrocephalosyndactyly, Type I . Acrocephalosyndactyly, Type II . Acrocephalosyndactyly, Type III . Acrocephalosyndactyly, Type V . Acrocephaly, Skull Asymmetry, and Mild Syndactyly . Apert-Crouzon Disease . Chotzen Syndrome . Craniofacial-Skeletal-Dermatologic Dysplasia . Dysostosis Craniofacialis with Hypertelorism . Kurczynski Casperson Syndrome . Noack Syndrome . Syndactylic Oxycephaly . Acrocephalosyndactylias . Acrocephalosyndactylies, Type 1 . Acrocephalosyndactylies, Type 3 . Acrocephalosyndactylies, Type I . Acrocephalosyndactylies, Type II . Acrocephalosyndactylies, Type III . Acrocephalosyndactylies, Type V . Acrocephalosyndactyly IIIs . Apert Crouzon Disease . Disease, Apert-Crouzon . Noack Syndromes . Saethre Chotzen Syndrome . Syndactylic Oxycephalies . Syndrome, Apert . Syndrome, Chotzen . Syndrome, Kurczynski Casperson . Syndrome, Noack . Syndrome, Pfeiffer . Syndrome, Saethre-Chotzen . Syndromes, Noack . Type I Acrocephalosyndactylies . Type I Acrocephalosyndactyly . Type II Acrocephalosyndactylies . Type II Acrocephalosyndactyly . Type III Acrocephalosyndactyly . Type V Acrocephalosyndactylies . Type V Acrocephalosyndactyly . Apert Syndrome . Pfeiffer Syndrome . Saethre-Chotzen Syndrome . 1.00
Prodromal Symptoms . Prodromal Characteristics . Prodromal Period . Prodromal Signs . Prodromal Stage . Prodromal States . Prodromal Syndromes . Characteristic, Prodromal . Characteristics, Prodromal . Period, Prodromal . Periods, Prodromal . Prodromal Characteristic . Prodromal Periods . Prodromal Sign . Prodromal Stages . Prodromal State . Prodromal Symptom . Prodromal Syndrome . Sign, Prodromal . Signs, Prodromal . Stage, Prodromal . Stages, Prodromal . State, Prodromal . States, Prodromal . Symptom, Prodromal . Symptoms, Prodromal . Syndrome, Prodromal . Syndromes, Prodromal . 0.45
Wolf-Hirschhorn Syndrome . 4p Deletion Syndrome . 4p- Syndrome . Chromosome 4p Deletion Syndrome . Chromosome 4p Monosomy . Chromosome 4p Syndrome . Del(4p) Syndrome . Mental Retardation, Unusual Facies, And Intrauterine Growth Retardation . Partial Monosomy 4p . Pitt Syndrome . Pitt-Rogers-Danks Syndrome . Wolf Syndrome . Wolf-Hirchhorn Syndrome . 4p Syndrome, Chromosome . 4p Syndromes, Chromosome . Chromosome 4p Syndromes . Pitt Rogers Danks Syndrome . Pitt Syndromes . Syndrome, Chromosome 4p . Syndrome, Pitt . Syndrome, Pitt-Rogers-Danks . Syndrome, Wolf . Syndrome, Wolf-Hirchhorn . Syndrome, Wolf-Hirschhorn . Syndromes, Chromosome 4p . Syndromes, Pitt . Wolf Hirchhorn Syndrome . Wolf Hirschhorn Syndrome . Wolf-Hirchhorn Syndrome . 0.45