Categorias DeCS
C10 Nervous System Diseases .
C10.228 Central Nervous System Diseases .
C10.228.140 Brain Diseases .
C10.228.140.380 Dementia .
C10.228.140.380.132 Aphasia, Primary Progressive .
C10.228.140.380.132.600 Primary Progressive Nonfluent Aphasia .
C10.228.140.380.266 Frontotemporal Lobar Degeneration .
C10.228.140.380.266.600 Primary Progressive Nonfluent Aphasia .
C10.574 Neurodegenerative Diseases .
C10.574.950 TDP-43 Proteinopathies .
C10.574.950.300 Frontotemporal Lobar Degeneration .
C10.574.950.300.600 Primary Progressive Nonfluent Aphasia .
C10.597 Neurologic Manifestations .
C10.597.606 Neurobehavioral Manifestations .
C10.597.606.150 Communication Disorders .
C10.597.606.150.500 Language Disorders .
C10.597.606.150.500.800 Speech Disorders .
C10.597.606.150.500.800.100 Aphasia .
C10.597.606.150.500.800.100.155 Aphasia, Primary Progressive .
C10.597.606.150.500.800.100.155.600 Primary Progressive Nonfluent Aphasia .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.131 Congenital Abnormalities .
C16.131.077 Abnormalities, Multiple .
C16.131.077.944 Wolf-Hirschhorn Syndrome .
C16.131.260 Chromosome Disorders .
C16.131.260.985 Wolf-Hirschhorn Syndrome .
C16.320 Genetic Diseases, Inborn .
C16.320.180 Chromosome Disorders .
C16.320.180.985 Wolf-Hirschhorn Syndrome .
C16.320.850 Skin Diseases, Genetic .
C16.320.850.368 Hyalinosis, Systemic .
C17 Skin and Connective Tissue Diseases .
C17.800 Skin Diseases .
C17.800.827 Skin Diseases, Genetic .
C17.800.827.384 Hyalinosis, Systemic .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.845 Proteostasis Deficiencies .
C18.452.845.800 TDP-43 Proteinopathies .
C18.452.845.800.300 Frontotemporal Lobar Degeneration .
C18.452.845.800.300.600 Primary Progressive Nonfluent Aphasia .
C23 Pathological Conditions, Signs and Symptoms .
C23.550 Pathologic Processes .
C23.550.288 Disease .
C23.550.288.500 Syndrome .
C23.888 Signs and Symptoms .
C23.888.592 Neurologic Manifestations .
C23.888.592.604 Neurobehavioral Manifestations .
C23.888.592.604.150 Communication Disorders .
C23.888.592.604.150.500 Language Disorders .
C23.888.592.604.150.500.800 Speech Disorders .
C23.888.592.604.150.500.800.100 Aphasia .
C23.888.592.604.150.500.800.100.155 Aphasia, Primary Progressive .
C23.888.592.604.150.500.800.100.155.600 Primary Progressive Nonfluent Aphasia .
C23.888.672 Prodromal Symptoms .
E01 Diagnosis .
E01.599 Prodromal Symptoms .
F03 Mental Disorders .
F03.615 Neurocognitive Disorders .
F03.615.400 Dementia .
F03.615.400.125 Aphasia, Primary Progressive .
F03.615.400.125.600 Primary Progressive Nonfluent Aphasia .
F03.615.400.380 Frontotemporal Lobar Degeneration .
F03.615.400.380.600 Primary Progressive Nonfluent Aphasia .
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| | Termos Sinônimos e Históricos | Documentos LILACS e MDL | |
| Wolf-Hirschhorn Syndrome . 4p Deletion Syndrome . 4p- Syndrome . Chromosome 4p Deletion Syndrome . Chromosome 4p Monosomy . Chromosome 4p Syndrome . Del(4p) Syndrome . Mental Retardation, Unusual Facies, And Intrauterine Growth Retardation . Partial Monosomy 4p . Pitt Syndrome . Pitt-Rogers-Danks Syndrome . Wolf Syndrome . Wolf-Hirchhorn Syndrome . 4p Syndrome, Chromosome . 4p Syndromes, Chromosome . Chromosome 4p Syndromes . Pitt Rogers Danks Syndrome . Pitt Syndromes . Syndrome, Chromosome 4p . Syndrome, Pitt . Syndrome, Pitt-Rogers-Danks . Syndrome, Wolf . Syndrome, Wolf-Hirchhorn . Syndrome, Wolf-Hirschhorn . Syndromes, Chromosome 4p . Syndromes, Pitt . Wolf Hirchhorn Syndrome . Wolf Hirschhorn Syndrome . Wolf-Hirchhorn Syndrome . 1.00
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| Prodromal Symptoms . Prodromal Characteristics . Prodromal Period . Prodromal Signs . Prodromal Stage . Prodromal States . Prodromal Syndromes . Characteristic, Prodromal . Characteristics, Prodromal . Period, Prodromal . Periods, Prodromal . Prodromal Characteristic . Prodromal Periods . Prodromal Sign . Prodromal Stages . Prodromal State . Prodromal Symptom . Prodromal Syndrome . Sign, Prodromal . Signs, Prodromal . Stage, Prodromal . Stages, Prodromal . State, Prodromal . States, Prodromal . Symptom, Prodromal . Symptoms, Prodromal . Syndrome, Prodromal . Syndromes, Prodromal . 0.61
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| Hyalinosis, Systemic . Fibromatosis Hyalinica Multiplex Juvenilis . Fibromatosis Juvenile Hyaline . Fibromatosis, Juvenile Hyaline . Hyaline Fibromatosis Juvenile . Hyaline Fibromatosis Syndrome . Hyalinosis, Systemic Juvenile . Infantile Systemic Hyalinosis . Juvenile Hyaline Fibromatosis . Juvenile Hyalinosis . Murray Syndrome . Puretic Syndrome . Systemic Hyalinosis . Fibromatosis Syndrome, Hyaline . Fibromatosis Syndromes, Hyaline . Hyaline Fibromatosis Syndromes . Hyaline Fibromatosis, Juvenile . Hyalinoses, Infantile Systemic . Hyalinoses, Juvenile . Hyalinoses, Systemic . Hyalinoses, Systemic Juvenile . Hyalinosis, Infantile Systemic . Hyalinosis, Juvenile . Infantile Systemic Hyalinoses . Juvenile Hyaline Fibromatoses . Juvenile Hyalinoses . Juvenile Hyalinoses, Systemic . Juvenile Hyalinosis, Systemic . Puretic Syndromes . Syndrome, Hyaline Fibromatosis . Syndrome, Murray . Syndrome, Puretic . Syndromes, Hyaline Fibromatosis . Syndromes, Puretic . Systemic Hyalinoses . Systemic Hyalinoses, Infantile . Systemic Hyalinosis, Infantile . Systemic Juvenile Hyalinoses . Systemic Juvenile Hyalinosis . 0.58
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