Categorias DeCS
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.202 Carbohydrate Metabolism, Inborn Errors .
C16.320.565.202.715 Mucopolysaccharidoses .
C16.320.565.202.715.650 Mucopolysaccharidosis III .
C16.320.565.595 Lysosomal Storage Diseases .
C16.320.565.595.600 Mucopolysaccharidoses .
C16.320.565.595.600.650 Mucopolysaccharidosis III .
C17 Skin and Connective Tissue Diseases .
C17.300 Connective Tissue Diseases .
C17.300.550 Mucinoses .
C17.300.550.575 Mucopolysaccharidoses .
C17.300.550.575.650 Mucopolysaccharidosis III .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.202 Carbohydrate Metabolism, Inborn Errors .
C18.452.648.202.715 Mucopolysaccharidoses .
C18.452.648.202.715.650 Mucopolysaccharidosis III .
C18.452.648.595 Lysosomal Storage Diseases .
C18.452.648.595.600 Mucopolysaccharidoses .
C18.452.648.595.600.650 Mucopolysaccharidosis III .
D08 Enzymes and Coenzymes .
D08.244 Cytochromes .
D08.244.175 Cytochrome a Group .
D08.244.175.600 Cytochromes a3 .
D12 Amino Acids, Peptides, and Proteins .
D12.644 Peptides .
D12.644.276 Intercellular Signaling Peptides and Proteins .
D12.644.276.374 Cytokines .
D12.644.276.374.200 Chemokines .
D12.644.276.374.200.120 Chemokines, CXC .
D12.644.276.374.200.120.600 Chemokine CXCL12 .
D12.776 Proteins .
D12.776.422 Hemeproteins .
D12.776.422.220 Cytochromes .
D12.776.422.220.175 Cytochrome a Group .
D12.776.422.220.175.600 Cytochromes a3 .
D12.776.467 Intercellular Signaling Peptides and Proteins .
D12.776.467.374 Cytokines .
D12.776.467.374.200 Chemokines .
D12.776.467.374.200.120 Chemokines, CXC .
D12.776.467.374.200.120.600 Chemokine CXCL12 .
D23 Biological Factors .
D23.125 Chemotactic Factors .
D23.125.300 Chemokines .
D23.125.300.120 Chemokines, CXC .
D23.125.300.120.600 Chemokine CXCL12 .
D23.469 Inflammation Mediators .
D23.469.200 Chemokines .
D23.469.200.120 Chemokines, CXC .
D23.469.200.120.600 Chemokine CXCL12 .
D23.529 Intercellular Signaling Peptides and Proteins .
D23.529.374 Cytokines .
D23.529.374.200 Chemokines .
D23.529.374.200.120 Chemokines, CXC .
D23.529.374.200.120.600 Chemokine CXCL12 .
E05 Investigative Techniques .
E05.196 Chemistry Techniques, Analytical .
E05.196.155 Chemical Fractionation .
E05.196.155.500 Fractionation, Field Flow .
E05.318 Epidemiologic Methods .
E05.318.308 Data Collection .
E05.318.308.980 Surveys and Questionnaires .
E05.318.308.980.438 Health Surveys .
E05.318.308.980.438.475 Health Status Indicators .
E05.318.308.980.438.475.456 Patient Acuity .
E05.318.308.980.438.475.456.500 Severity of Illness Index .
E05.318.308.980.438.475.456.500.750 Simplified Acute Physiology Score .
N05 Health Care Quality, Access, and Evaluation .
N05.715 Quality of Health Care .
N05.715.360 Health Care Evaluation Mechanisms .
N05.715.360.300 Data Collection .
N05.715.360.300.800 Surveys and Questionnaires .
N05.715.360.300.800.438 Health Surveys .
N05.715.360.300.800.438.375 Health Status Indicators .
N05.715.360.300.800.438.375.364 Patient Acuity .
N05.715.360.300.800.438.375.364.500 Severity of Illness Index .
N05.715.360.300.800.438.375.364.500.750 Simplified Acute Physiology Score .
N06 Environment and Public Health .
N06.850 Public Health .
N06.850.520 Epidemiologic Methods .
N06.850.520.308 Data Collection .
N06.850.520.308.980 Surveys and Questionnaires .
N06.850.520.308.980.438 Health Surveys .
N06.850.520.308.980.438.475 Health Status Indicators .
N06.850.520.308.980.438.475.364 Patient Acuity .
N06.850.520.308.980.438.475.364.500 Severity of Illness Index .
N06.850.520.308.980.438.475.364.500.750 Simplified Acute Physiology Score .
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| | Termos Sinônimos e Históricos | Documentos LILACS e MDL | | | | |
| Mucopolysaccharidosis III . Acetyl-CoA:alpha-Glucosaminide N-Acetyltransferase Deficiency . Heparan Sulfate Sulfatase Deficiency . MPS 3 A . MPS 3 B . MPS 3 C . MPS 3 D . MPS III A . MPS III B . MPS III C . MPS III D . MPS IIIA . MPS IIIB . MPS IIIC . MPS IIID . MPS3A . MPS3B . MPS3C . Mucopolysaccharidosis 3 . Mucopolysaccharidosis Type 3 A . Mucopolysaccharidosis Type 3 A Sanfilippo Syndrome . Mucopolysaccharidosis Type 3 B . Mucopolysaccharidosis Type 3 C . Mucopolysaccharidosis Type 3 D . Mucopolysaccharidosis Type IIIA . Mucopolysaccharidosis Type IIIB . Mucopolysaccharidosis Type IIIC . Mucopolysaccharidosis Type IIID . N-Acetyl-alpha-D-Glucosaminidase Deficiency . N-Acetylglucosamine-6-Sulfatase Deficiency . N-Acetylglucosamine-6-Sulfate Sulfatase Deficiency . NAGLU Deficiency . San Filippo's Syndrome . Sanfilippo Syndrome . Sanfilippo Syndrome A . Sanfilippo Syndrome B . Sanfilippo Syndrome C . Sanfilippo Syndrome D . Sulfamidase Deficiency . Acetyl CoA:alpha Glucosaminide N Acetyltransferase Deficiency . Acetyl-CoA:alpha-Glucosaminide N-Acetyltransferase Deficiencies . Deficiencies, Acetyl-CoA:alpha-Glucosaminide N-Acetyltransferase . Deficiencies, N-Acetyl-alpha-D-Glucosaminidase . Deficiencies, N-Acetylglucosamine-6-Sulfatase . Deficiencies, N-Acetylglucosamine-6-Sulfate Sulfatase . Deficiencies, NAGLU . Deficiencies, Sulfamidase . Deficiency, Acetyl-CoA:alpha-Glucosaminide N-Acetyltransferase . Deficiency, N-Acetyl-alpha-D-Glucosaminidase . Deficiency, N-Acetylglucosamine-6-Sulfatase . Deficiency, N-Acetylglucosamine-6-Sulfate Sulfatase . Deficiency, NAGLU . Deficiency, Sulfamidase . MPS IIIDs . Mucopolysaccharidosis IIIs . Mucopolysaccharidosis Type IIIAs . Mucopolysaccharidosis Type IIIBs . Mucopolysaccharidosis Type IIICs . Mucopolysaccharidosis Type IIIDs . N Acetyl alpha D Glucosaminidase Deficiency . N Acetylglucosamine 6 Sulfatase Deficiency . N Acetylglucosamine 6 Sulfate Sulfatase Deficiency . N-Acetyl-alpha-D-Glucosaminidase Deficiencies . N-Acetylglucosamine-6-Sulfatase Deficiencies . N-Acetylglucosamine-6-Sulfate Sulfatase Deficiencies . N-Acetyltransferase Deficiencies, Acetyl-CoA:alpha-Glucosaminide . N-Acetyltransferase Deficiency, Acetyl-CoA:alpha-Glucosaminide . NAGLU Deficiencies . Oligophrenia, Polydystrophic . Oligophrenias, Polydystrophic . Polydystrophic Oligophrenias . San Filippo Syndrome . San Filippos Syndrome . Sanfilippo Syndromes . Sanfilippos Syndrome . Sulfamidase Deficiencies . Sulfatase Deficiencies, N-Acetylglucosamine-6-Sulfate . Sulfatase Deficiency, N-Acetylglucosamine-6-Sulfate . Syndrome, San Filippo's . Syndrome, Sanfilippo . Syndrome, Sanfilippo's . Syndromes, Sanfilippo . Polydystrophic Oligophrenia . Sanfilippo's Syndrome . 0.50
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