Categorias DeCS
C10 Nervous System Diseases .
C10.228 Central Nervous System Diseases .
C10.228.140 Brain Diseases .
C10.228.140.163 Brain Diseases, Metabolic .
C10.228.140.163.100 Brain Diseases, Metabolic, Inborn .
C10.228.140.163.100.435 Lysosomal Storage Diseases, Nervous System .
C10.228.140.163.100.435.825 Sphingolipidoses .
C10.228.140.163.100.435.825.300 Gangliosidoses .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.189 Brain Diseases, Metabolic, Inborn .
C16.320.565.189.435 Lysosomal Storage Diseases, Nervous System .
C16.320.565.189.435.825 Sphingolipidoses .
C16.320.565.189.435.825.300 Gangliosidoses .
C16.320.565.398 Lipid Metabolism, Inborn Errors .
C16.320.565.398.641 Lipidoses .
C16.320.565.398.641.803 Sphingolipidoses .
C16.320.565.398.641.803.350 Gangliosidoses .
C16.320.565.595 Lysosomal Storage Diseases .
C16.320.565.595.554 Lysosomal Storage Diseases, Nervous System .
C16.320.565.595.554.825 Sphingolipidoses .
C16.320.565.595.554.825.300 Gangliosidoses .
C16.320.565.618 Metal Metabolism, Inborn Errors .
C16.320.565.618.337 Hemochromatosis .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.132 Brain Diseases, Metabolic .
C18.452.132.100 Brain Diseases, Metabolic, Inborn .
C18.452.132.100.435 Lysosomal Storage Diseases, Nervous System .
C18.452.132.100.435.825 Sphingolipidoses .
C18.452.132.100.435.825.300 Gangliosidoses .
C18.452.565 Iron Metabolism Disorders .
C18.452.565.500 Iron Overload .
C18.452.565.500.480 Hemochromatosis .
C18.452.584 Lipid Metabolism Disorders .
C18.452.584.687 Lipidoses .
C18.452.584.687.803 Sphingolipidoses .
C18.452.584.687.803.350 Gangliosidoses .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.189 Brain Diseases, Metabolic, Inborn .
C18.452.648.189.435 Lysosomal Storage Diseases, Nervous System .
C18.452.648.189.435.825 Sphingolipidoses .
C18.452.648.189.435.825.300 Gangliosidoses .
C18.452.648.398 Lipid Metabolism, Inborn Errors .
C18.452.648.398.641 Lipidoses .
C18.452.648.398.641.803 Sphingolipidoses .
C18.452.648.398.641.803.350 Gangliosidoses .
C18.452.648.595 Lysosomal Storage Diseases .
C18.452.648.595.554 Lysosomal Storage Diseases, Nervous System .
C18.452.648.595.554.825 Sphingolipidoses .
C18.452.648.595.554.825.300 Gangliosidoses .
C18.452.648.618 Metal Metabolism, Inborn Errors .
C18.452.648.618.337 Hemochromatosis .
D09 Carbohydrates .
D09.400 Glycoconjugates .
D09.400.410 Glycolipids .
D09.400.410.420 Glycosphingolipids .
D09.400.410.420.025 Acidic Glycosphingolipids .
D09.400.410.420.025.475 Gangliosides .
D10 Lipids .
D10.390 Glycolipids .
D10.390.470 Glycosphingolipids .
D10.390.470.025 Acidic Glycosphingolipids .
D10.390.470.025.475 Gangliosides .
D10.570 Membrane Lipids .
D10.570.877 Sphingolipids .
D10.570.877.360 Glycosphingolipids .
D10.570.877.360.025 Acidic Glycosphingolipids .
D10.570.877.360.025.475 Gangliosides .
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| | Termos Sinônimos e Históricos | Documentos LILACS e MDL | | | | | | | |
| Hemochromatosis . Bronze Diabetes . Bronzed Cirrhosis . Familial Hemochromatosis . Genetic Hemochromatosis . Haemochromatosis . Hemochromatoses . Iron Storage Disorder . Pigmentary Cirrhosis . Primary Hemochromatosis . Troisier-Hanot-Chauffard Syndrome . Von Recklenhausen-Applebaum Disease . Bronzed Cirrhoses . Cirrhoses, Bronzed . Cirrhoses, Pigmentary . Cirrhosis, Bronzed . Cirrhosis, Pigmentary . Disease, Von Recklenhausen-Applebaum . Diseases, Von Recklenhausen-Applebaum . Disorder, Iron Storage . Disorders, Iron Storage . Familial Hemochromatoses . Genetic Hemochromatoses . Haemochromatoses . Hemochromatose . Hemochromatoses, Familial . Hemochromatoses, Genetic . Hemochromatosis, Familial . Hemochromatosis, Genetic . Iron Storage Disorders . Pigmentary Cirrhoses . Recklenhausen-Applebaum Disease, Von . Recklenhausen-Applebaum Diseases, Von . Storage Disorder, Iron . Storage Disorders, Iron . Syndrome, Troisier-Hanot-Chauffard . Syndromes, Troisier-Hanot-Chauffard . Troisier Hanot Chauffard Syndrome . Troisier-Hanot-Chauffard Syndromes . Von Recklenhausen Applebaum Disease . Von Recklenhausen-Applebaum Diseases . Diabetes, Bronze . 0.60
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