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 Categorias DeCS

C10 Nervous System Diseases .
C10.228 Central Nervous System Diseases .
C10.228.140 Brain Diseases .
C10.228.140.079 Basal Ganglia Diseases .
C10.228.140.079.882 Supranuclear Palsy, Progressive .
C10.228.140.163 Brain Diseases, Metabolic .
C10.228.140.163.100 Brain Diseases, Metabolic, Inborn .
C10.228.140.163.100.435 Lysosomal Storage Diseases, Nervous System .
C10.228.140.163.100.435.825 Sphingolipidoses .
C10.228.140.163.100.435.825.700 Niemann-Pick Diseases .
C10.228.140.163.100.435.825.700.500 Niemann-Pick Disease, Type A .
C10.228.662 Movement Disorders .
C10.228.662.700 Supranuclear Palsy, Progressive .
C10.292 Cranial Nerve Diseases .
C10.292.562 Ocular Motility Disorders .
C10.292.562.750 Ophthalmoplegia .
C10.292.562.750.500 Supranuclear Palsy, Progressive .
C10.574 Neurodegenerative Diseases .
C10.574.945 Tauopathies .
C10.574.945.500 Supranuclear Palsy, Progressive .
C10.597 Neurologic Manifestations .
C10.597.622 Paralysis .
C10.597.622.447 Ophthalmoplegia .
C10.597.622.447.690 Supranuclear Palsy, Progressive .
C11 Eye Diseases .
C11.590 Ocular Motility Disorders .
C11.590.472 Ophthalmoplegia .
C11.590.472.500 Supranuclear Palsy, Progressive .
C15 Hemic and Lymphatic Diseases .
C15.604 Lymphatic Diseases .
C15.604.250 Histiocytosis .
C15.604.250.410 Histiocytosis, Non-Langerhans-Cell .
C15.604.250.410.625 Niemann-Pick Diseases .
C15.604.250.410.625.500 Niemann-Pick Disease, Type A .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.189 Brain Diseases, Metabolic, Inborn .
C16.320.565.189.435 Lysosomal Storage Diseases, Nervous System .
C16.320.565.189.435.825 Sphingolipidoses .
C16.320.565.189.435.825.700 Niemann-Pick Diseases .
C16.320.565.189.435.825.700.500 Niemann-Pick Disease, Type A .
C16.320.565.398 Lipid Metabolism, Inborn Errors .
C16.320.565.398.641 Lipidoses .
C16.320.565.398.641.803 Sphingolipidoses .
C16.320.565.398.641.803.730 Niemann-Pick Diseases .
C16.320.565.398.641.803.730.500 Niemann-Pick Disease, Type A .
C16.320.565.595 Lysosomal Storage Diseases .
C16.320.565.595.554 Lysosomal Storage Diseases, Nervous System .
C16.320.565.595.554.825 Sphingolipidoses .
C16.320.565.595.554.825.700 Niemann-Pick Diseases .
C16.320.565.595.554.825.700.500 Niemann-Pick Disease, Type A .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.132 Brain Diseases, Metabolic .
C18.452.132.100 Brain Diseases, Metabolic, Inborn .
C18.452.132.100.435 Lysosomal Storage Diseases, Nervous System .
C18.452.132.100.435.825 Sphingolipidoses .
C18.452.132.100.435.825.700 Niemann-Pick Diseases .
C18.452.132.100.435.825.700.500 Niemann-Pick Disease, Type A .
C18.452.584 Lipid Metabolism Disorders .
C18.452.584.687 Lipidoses .
C18.452.584.687.803 Sphingolipidoses .
C18.452.584.687.803.730 Niemann-Pick Diseases .
C18.452.584.687.803.730.500 Niemann-Pick Disease, Type A .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.189 Brain Diseases, Metabolic, Inborn .
C18.452.648.189.435 Lysosomal Storage Diseases, Nervous System .
C18.452.648.189.435.825 Sphingolipidoses .
C18.452.648.189.435.825.700 Niemann-Pick Diseases .
C18.452.648.189.435.825.700.500 Niemann-Pick Disease, Type A .
C18.452.648.398 Lipid Metabolism, Inborn Errors .
C18.452.648.398.641 Lipidoses .
C18.452.648.398.641.803 Sphingolipidoses .
C18.452.648.398.641.803.730 Niemann-Pick Diseases .
C18.452.648.398.641.803.730.500 Niemann-Pick Disease, Type A .
C18.452.648.595 Lysosomal Storage Diseases .
C18.452.648.595.554 Lysosomal Storage Diseases, Nervous System .
C18.452.648.595.554.825 Sphingolipidoses .
C18.452.648.595.554.825.700 Niemann-Pick Diseases .
C18.452.648.595.554.825.700.500 Niemann-Pick Disease, Type A .
C23 Pathological Conditions, Signs and Symptoms .
C23.888 Signs and Symptoms .
C23.888.592 Neurologic Manifestations .
C23.888.592.636 Paralysis .
C23.888.592.636.447 Ophthalmoplegia .
C23.888.592.636.447.690 Supranuclear Palsy, Progressive .
 
 Termos
 Sinônimos e Históricos
Documentos
LILACS e MDL
 
Niemann-Pick Disease, Type A .
Classical Niemann-Pick Disease .
Neuronal Cholesterol Lipidosis .
Niemann-Pick Disease, Acute Neuronopathic Form .
Niemann-Pick Disease, Acute Neurovisceral Form .
Niemann-Pick Disease, Neuronopathic Type .
Niemann-Pick's Disease Type A .
Ophthalmoplegia, Supraoptic Vertical .
Sphingomyelin Cholesterol Lipidosis .
Sphingomyelin Lipidosis .
Sphingomyelinase Deficiency .
Type A Niemann-Pick Disease .
Cholesterol Lipidoses, Neuronal .
Cholesterol Lipidoses, Sphingomyelin .
Cholesterol Lipidosis, Neuronal .
Cholesterol Lipidosis, Sphingomyelin .
Classical Niemann Pick Disease .
Deficiencies, Sphingomyelinase .
Deficiency, Sphingomyelinase .
Lipidoses, Neuronal Cholesterol .
Lipidoses, Sphingomyelin .
Lipidoses, Sphingomyelin Cholesterol .
Lipidosis, Neuronal Cholesterol .
Lipidosis, Sphingomyelin .
Lipidosis, Sphingomyelin Cholesterol .
Neuronal Cholesterol Lipidoses .
Niemann Pick Disease, Acute Neuronopathic Form .
Niemann Pick Disease, Acute Neurovisceral Form .
Niemann Pick Disease, Neuronopathic Type .
Niemann Pick Disease, Type A .
Niemann Pick's Disease Type A .
Niemann-Pick Disease, Classical .
Ophthalmoplegias, Supraoptic Vertical .
Sphingomyelin Cholesterol Lipidoses .
Sphingomyelin Lipidoses .
Sphingomyelinase Deficiencies .
Sphingomyelinase Deficiency Diseases .
Supraoptic Vertical Ophthalmoplegia .
Supraoptic Vertical Ophthalmoplegias .
Type A Niemann Pick Disease .
Vertical Ophthalmoplegia, Supraoptic .
Vertical Ophthalmoplegias, Supraoptic .
Sphingomyelinase Deficiency Disease .
Classical Niemann-Pick Disease .
1.00
 
Niemann-Pick Diseases .
Niemann Pick Disease .
Niemann Pick Diseases .
Niemann-Pick Disease .
Lipidosis, Neuronal Cholesterol .
Ophthalmoplegia, Supraoptic Vertical .
HISTIOCYTOSIS, LIPID .
0.96
 
Ophthalmoplegia .
External Ophthalmoplegia .
Internal Ophthalmoplegia .
Ophthalmoparesis .
External Ophthalmoplegias .
Internal Ophthalmoplegias .
Ophthalmopareses .
Ophthalmoplegia, External .
Ophthalmoplegia, Internal .
Ophthalmoplegias .
Ophthalmoplegias, External .
Ophthalmoplegias, Internal .
Paralysis, Oculomotor .
Oculomotor Paralysis .
0.67
 
Supranuclear Palsy, Progressive .
Palsy, Progressive Supranuclear .
Progressive Supranuclear Palsy .
Richardson's Syndrome .
Steele-Richardson-Olszewski Disease .
Supranuclear Palsy, Progressive, 1 .
Progressive Supranuclear Palsies .
Richardson Syndrome .
Steele Richardson Olszewski Disease .
Steele Richardson Olszewski Syndrome .
Supranuclear Ophthalmoplegia, Progressive .
Supranuclear Palsies, Progressive .
Syndrome, Richardson's .
Syndrome, Steele-Richardson-Olszewski .
Steele-Richardson-Olszewski Syndrome .
Ophthalmoplegia, Progressive Supranuclear .
Progressive Supranuclear Ophthalmoplegia .
PALSY, PROGRESSIVE SUPRANUCLEAR .
0.58