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 DeCS Categories

C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.202 Carbohydrate Metabolism, Inborn Errors .
C16.320.565.202.715 Mucopolysaccharidoses .
C16.320.565.202.715.640 Mucopolysaccharidosis I .
C16.320.565.595 Lysosomal Storage Diseases .
C16.320.565.595.600 Mucopolysaccharidoses .
C16.320.565.595.600.640 Mucopolysaccharidosis I .
C17 Skin and Connective Tissue Diseases .
C17.300 Connective Tissue Diseases .
C17.300.550 Mucinoses .
C17.300.550.575 Mucopolysaccharidoses .
C17.300.550.575.640 Mucopolysaccharidosis I .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.202 Carbohydrate Metabolism, Inborn Errors .
C18.452.648.202.715 Mucopolysaccharidoses .
C18.452.648.202.715.640 Mucopolysaccharidosis I .
C18.452.648.595 Lysosomal Storage Diseases .
C18.452.648.595.600 Mucopolysaccharidoses .
C18.452.648.595.600.640 Mucopolysaccharidosis I .
D01 Inorganic Chemicals .
D01.210 Chlorine Compounds .
D01.210.465 Hypochlorous Acid .
D01.210.465.800 Sodium Hypochlorite .
D01.248 Electrolytes .
D01.248.497 Ions 5743 .
D01.248.497.158 Anions .
D01.248.497.158.750 Phosphites .
D01.650 Oxygen Compounds .
D01.650.550 Oxides .
D01.650.550.400 Hypochlorous Acid .
D01.650.550.400.800 Sodium Hypochlorite .
D01.695 Phosphorus Compounds .
D01.695.625 Phosphorus Acids .
D01.695.625.700 Phosphorous Acids .
D01.695.625.700.675 Phosphites .
D01.857 Sodium Compounds .
D01.857.750 Sodium Hypochlorite .
D02 Organic Chemicals .
D02.092 Amines .
D03 Heterocyclic Compounds .
D03.633 Heterocyclic Compounds, Fused-Ring .
D03.633.100 Heterocyclic Compounds, 2-Ring .
D03.633.100.759 Purines .
D03.633.100.759.138 Adenine .
D03.633.100.759.138.525 Cytokinins .
D03.633.100.759.138.525.700 Zeatin .
D09 Carbohydrates .
D09.698 Polysaccharides .
D09.698.373 Glycosaminoglycans .
D09.698.373.200 Chondroitin .
SP4 Environmental Health .
SP4.011 Science .
SP4.011.097 Chemistry .
SP4.011.097.036 Organic Chemicals .
SP4.011.097.036.604 Amines .
SP4.011.097.039 Chemical Compounds .
SP4.011.097.039.739 Chlorine Compounds .
SP4.011.097.039.739.480 Sodium Hypochlorite .
 
 Terms
 Synonyms & Historicals
Documents
LILACS e MDL
 
Chondroitin .
A mucopolysaccharide constituent of chondrin. (Grant & Hackh's Chemical Dictionary, 5th ed) .
1.00
92791
 
Zeatin .
An aminopurine factor in plant extracts that induces cell division. (Grant & Hackh's Chemical Dict, 5th ed) .
0.49
0236
 
Amines .
A group of compounds derived from ammonia by substituting organic radicals for the hydrogens. (From Grant & Hackh's Chemical Dictionary, 5th ed) .
0.47
4322854
 
Sodium Hypochlorite .
Antiformin .
Clorox .
Sodium Hypochlorite (Solution) .
Hypochlorite, Sodium .
It is used as an oxidizing and bleaching agent and as a disinfectant. (From Grant & Hackh's Chemical Dictionary, 5th ed) .
0.46
5514150
 
Glycosaminoglycans .
Mucopolysaccharides .
Heteropolysaccharides which contain an N-acetylated hexosamine in a characteristic repeating disaccharide unit. The repeating structure of each disaccharide involves alternate 1,4- and 1,3-linkages consisting of either N-acetylglucosamine (see ACETYLGLUCOSAMINE) or N-acetylgalactosamine (see ACETYLGALACTOSAMINE). .
0.44
18221610
 
Phosphites .
Inorganic salts or organic esters of phosphorous acid that contain the (3-)PO3 radical. (From Grant & Hackh's Chemical Dictionary, 5th ed) .
0.42
3394
 
Mucopolysaccharidoses .
Mucopolysaccharidosis .
Group of lysosomal storage diseases each caused by an inherited deficiency of an enzyme involved in the degradation of glycosaminoglycans (mucopolysaccharides). The diseases are progressive and often display a wide spectrum of clinical severity within one enzyme deficiency. .
0.41
591960
 
Mucopolysaccharidosis I .
Gargoylism .
Gargoylism, Hurler Syndrome .
Hurler Disease .
Hurler Syndrome .
Hurler's Disease .
Mucopolysaccharidosis 1 .
Mucopolysaccharidosis 5 .
Mucopolysaccharidosis I-S .
Mucopolysaccharidosis Type I .
Mucopolysaccharidosis Type Ih .
Mucopolysaccharidosis Type Ih S .
Mucopolysaccharidosis Type Is .
Scheie Syndrome .
alpha-L-Iduronidase Deficiency .
Disease, Hurler's .
Gargoylisms .
Hurler Scheie Syndrome .
Hurler Syndrome Gargoylism .
Lipochondrodystrophies .
Mucopolysaccharidosis I S .
Mucopolysaccharidosis Is .
Mucopolysaccharidosis Type Ihs .
Syndrome, Hurler's .
Syndrome, Scheie's .
Type Ih, Mucopolysaccharidosis .
Type Ihs, Mucopolysaccharidosis .
alpha L Iduronidase Deficiency .
alpha-L-Iduronidase Deficiencies .
Hurler's Syndrome .
Pfaundler-Hurler Syndrome .
Lipochondrodystrophy .
Hurler-Scheie Syndrome .
Mucopolysaccharidosis V .
Scheie's Syndrome .
GARGOYLISM .
Systemic lysosomal storage disease caused by a deficiency of alpha-L-iduronidase (IDURONIDASE) and characterized by progressive physical deterioration with urinary excretion of DERMATAN SULFATE and HEPARAN SULFATE. There are three recognized phenotypes representing a spectrum of clinical severity from severe to mild: Hurler syndrome, Hurler-Scheie syndrome and Scheie syndrome (formerly mucopolysaccharidosis V). Symptoms may include DWARFISM; hepatosplenomegaly; thick, coarse facial features with low nasal bridge; corneal clouding; cardiac complications; and noisy breathing. .
0.41
311215