beta-Thalassemia. Erythroblastic Anemia . Mediterranean Anemia . Microcytemia, beta Type . Thalassemia Intermedia . Thalassemia Major (beta-Thalassemia Major) . Thalassemia Minor (beta-Thalassemia Minor) . Thalassemia, beta Type . beta Thalassemia . Anemia, Cooley . Anemia, Cooleys . Anemias, Erythroblastic . Anemias, Mediterranean . Cooley's Anemia . Disease, Hemoglobin F . Intermedia, Thalassemia . Intermedias, Thalassemia . Major, Thalassemia (beta-Thalassemia Major) . Majors, Thalassemia (beta-Thalassemia Major) . Mediterranean Anemias . Microcytemias, beta Type . Minor, Thalassemia (beta-Thalassemia Minor) . Minors, Thalassemia (beta-Thalassemia Minor) . Thalassemia Intermedias . Thalassemia Major (beta Thalassemia Major) . Thalassemia Majors (beta-Thalassemia Major) . Thalassemia Minor (beta Thalassemia Minor) . Thalassemia Minors (beta-Thalassemia Minor) . Thalassemia, beta . Thalassemias, beta . Thalassemias, beta Type . Type Microcytemia, beta . Type Microcytemias, beta . Type Thalassemia, beta . Type Thalassemias, beta . beta Thalassemias . beta Type Microcytemia . beta Type Microcytemias . beta Type Thalassemia . beta Type Thalassemias . Anemia, Cooley's . Anemia, Erythroblastic . Anemia, Mediterranean . Hemoglobin F Disease . Thalassemia Major . Thalassemia Minor . A disorder characterized by reduced synthesis of the beta chains of hemoglobin. There is retardation of hemoglobin A synthesis in the heterozygous form (thalassemia minor), which is asymptomatic, while in the homozygous form (thalassemia major, Cooley's anemia, Mediterranean anemia, erythroblastic anemia), which can result in severe complications and even death, hemoglobin A synthesis is absent. . 1.00
Anemia, Pernicious. Pernicious Anemia . Addison Anemia . Addisons Anemia . Anemia, Addison . Anemia, Addisons . Addison's Anemia . Anemia, Addison's . A megaloblastic anemia occurring in children but more commonly in later life, characterized by histamine-fast achlorhydria, in which the laboratory and clinical manifestations are based on malabsorption of vitamin B 12 due to a failure of the gastric mucosa to secrete adequate and potent intrinsic factor. (Dorland, 27th ed) . 0.54
Fanconi Anemia. Fanconi Hypoplastic Anemia . Fanconi Pancytopenia . Fanconi Panmyelopathy . Fanconi's Anemia . Anemia, Fanconi's . Anemias, Fanconi . Fanconi Anemias . Anemia, Fanconi . FANCONI'S ANEMIA . Congenital disorder affecting all bone marrow elements, resulting in ANEMIA; LEUKOPENIA; and THROMBOPENIA, and associated with cardiac, renal, and limb malformations as well as dermal pigmentary changes. Spontaneous CHROMOSOME BREAKAGE is a feature of this disease along with predisposition to LEUKEMIA. There are at least 7 complementation groups in Fanconi anemia: FANCA, FANCB, FANCC, FANCD1, FANCD2, FANCE, FANCF, FANCG, and FANCL. (from Online Mendelian Inheritance in Man, http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=227650, August 20, 2004) . 0.53