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 DeCS Categories

D05 Macromolecular Substances .
D05.500 Multiprotein Complexes .
D05.500.562 Multienzyme Complexes .
D05.500.562.468 Ketoglutarate Dehydrogenase Complex .
D08 Enzymes and Coenzymes .
D08.811 Enzymes .
D08.811.600 Multienzyme Complexes .
D08.811.600.465 Ketoglutarate Dehydrogenase Complex .
D08.811.682 Oxidoreductases .
D08.811.682.657 Oxidoreductases Acting on Aldehyde or Oxo Group Donors .
D08.811.682.657.350 Ketone Oxidoreductases .
D08.811.682.657.350.750 Ketoglutarate Dehydrogenase Complex .
D08.811.682.657.350.760 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) .
D08.811.682.657.350.825 2-Oxoisovalerate Dehydrogenase (Acylating) .
 
 Terms
 Synonyms & Historicals
Documents
LILACS e MDL
 
2-Oxoisovalerate Dehydrogenase (Acylating) .
2-Oxoisovalerate Dehydrogenase .
alpha-Ketoisovalerate Dehydrogenase .
2 Oxoisovalerate Dehydrogenase .
Dehydrogenase, 2-Oxoisovalerate .
Dehydrogenase, alpha-Ketoisovalerate .
alpha Ketoisovalerate Dehydrogenase .
An NAD+ dependent enzyme that catalyzes the oxidation 3-methyl-2-oxobutanoate to 2-methylpropanoyl-CoA. It plays a role in the degradation of VALINE; LEUCINE; and ISOLEUCINE. .
1.00
06
 
3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) .
2-Oxoisocaproate Dehydrogenase .
Alpha-Keto Acid Dehydrogenase .
BCKA Decarboxylase .
Branched Chain Alpha-Keto Acid Decarboxylase .
Branched Chain Ketoacid Dehydrogenase .
Branched-Chain 2-Oxo Acid Dehydrogenase .
Branched-Chain Keto Acid Dehydrogenase .
Branched-Chain Oxo-Acid Dehydrogenase .
2 Oxoisocaproate Dehydrogenase .
Acid Dehydrogenase, Alpha-Keto .
Alpha Keto Acid Dehydrogenase .
Branched Chain 2 Oxo Acid Dehydrogenase .
Branched Chain Alpha Keto Acid Decarboxylase .
Branched Chain Keto Acid Dehydrogenase .
Branched Chain Oxo Acid Dehydrogenase .
Decarboxylase, BCKA .
Dehydrogenase, 2-Oxoisocaproate .
Dehydrogenase, Alpha-Keto Acid .
Dehydrogenase, Branched-Chain Oxo-Acid .
Oxo-Acid Dehydrogenase, Branched-Chain .
2-Oxoisovalerate Dehydrogenase (Lipoamide) .
A ketone oxidoreductase that catalyzes the overall conversion of alpha-keto acids to ACYL-CoA and CO2. The enzyme requires THIAMINE DIPHOSPHATE as a cofactor. Defects in genes that code for subunits of the enzyme are a cause of MAPLE SYRUP URINE DISEASE. The enzyme was formerly classified as EC 1.2.4.3. .
0.84
0694
 
Ketoglutarate Dehydrogenase Complex .
2-Keto-4-Hydroxyglutarate Dehydrogenase .
2-Oxoglutarate Dehydrogenase .
2-Oxoglutarate Dehydrogenase Complex .
Oxoglutarate Dehydrogenase .
alpha-Ketoglutarate Dehydrogenase .
alpha-Ketoglutarate Dehydrogenase Complex .
2 Keto 4 Hydroxyglutarate Dehydrogenase .
2 Oxoglutarate Dehydrogenase .
2 Oxoglutarate Dehydrogenase Complex .
Complex, 2-Oxoglutarate Dehydrogenase .
Complex, Ketoglutarate Dehydrogenase .
Complex, alpha-Ketoglutarate Dehydrogenase .
Dehydrogenase Complex, 2-Oxoglutarate .
Dehydrogenase Complex, Ketoglutarate .
Dehydrogenase Complex, alpha-Ketoglutarate .
Dehydrogenase, 2-Keto-4-Hydroxyglutarate .
Dehydrogenase, 2-Oxoglutarate .
Dehydrogenase, Oxoglutarate .
Dehydrogenase, alpha-Ketoglutarate .
alpha Ketoglutarate Dehydrogenase .
alpha Ketoglutarate Dehydrogenase Complex .
0.75
0990