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 DeCS Categories

C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.202 Carbohydrate Metabolism, Inborn Errors .
C16.320.565.202.251 Fructose Metabolism, Inborn Errors .
C16.320.565.202.251.271 Fructose Intolerance .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.202 Carbohydrate Metabolism, Inborn Errors .
C18.452.648.202.251 Fructose Metabolism, Inborn Errors .
C18.452.648.202.251.271 Fructose Intolerance .
D08 Enzymes and Coenzymes .
D08.811 Enzymes .
D08.811.277 Hydrolases .
D08.811.277.352 Esterases .
D08.811.277.352.650 Phosphoric Monoester Hydrolases .
D08.811.277.352.650.200 Fructose-Bisphosphatase .
D09 Carbohydrates .
D09.067 Amino Sugars .
D09.067.342 Hexosamines .
D09.067.342.300 Fructosamine .
D09.698 Polysaccharides .
D09.698.350 Fructans .
D09.894 Sugar Phosphates .
D09.894.417 Hexosephosphates .
D09.894.417.313 Fructosephosphates .
D09.894.417.313.300 Fructosediphosphates .
D09.894.417.592 Hexosediphosphates .
D09.894.417.592.300 Fructosediphosphates .
D09.947 Sugars .
D09.947.875 Monosaccharides .
D09.947.875.359 Hexoses .
D09.947.875.359.250 Fructose .
D09.947.875.465 Ketoses .
D09.947.875.465.354 Fructose .
 
 Terms
 Synonyms & Historicals
Documents
LILACS e MDL
 
Fructose .
Apir Levulosa .
Fleboplast Levulosa .
Levulosa .
Levulosa Baxter .
Levulosa Braun .
Levulosa Grifols .
Levulosa Ibys .
Levulosa Ife .
Levulosa Mein .
Levulosado Bieffe Medit .
Levulosado Braun .
Levulosado Vitulia .
Plast Apyr Levulosa Mein .
Levulosa, Apir .
Levulosa, Fleboplast .
Levulose .
A monosaccharide in sweet fruits and honey that is soluble in water, alcohol, or ether. It is used as a preservative and an intravenous infusion in parenteral feeding. .
1.00
13714209
 
Fructose Intolerance .
ALDOB Deficiency .
Aldolase B Deficiency .
Fructose Aldolase B Deficiency .
Fructose Intolerance, Hereditary .
Fructose-1,6-Biphosphate Aldolase Deficiency .
Fructose-1,6-Bisphosphate Aldolase B Deficiency .
Fructose-1-Phosphate Aldolase Deficiency .
Fructosemia .
Hereditary Fructose Intolerance .
ALDOB Deficiencies .
Aldolase B Deficiencies .
Aldolase Deficiencies, Fructose-1,6-Biphosphate .
Aldolase Deficiencies, Fructose-1-Phosphate .
Aldolase Deficiency, Fructose-1,6-Biphosphate .
Aldolase Deficiency, Fructose-1-Phosphate .
Deficiencies, ALDOB .
Deficiencies, Aldolase B .
Deficiencies, Fructose-1,6-Biphosphate Aldolase .
Deficiencies, Fructose-1-Phosphate Aldolase .
Deficiency, ALDOB .
Deficiency, Aldolase B .
Deficiency, Fructose-1,6-Biphosphate Aldolase .
Deficiency, Fructose-1-Phosphate Aldolase .
Fructose 1 Phosphate Aldolase Deficiency .
Fructose 1,6 Biphosphate Aldolase Deficiency .
Fructose 1,6 Bisphosphate Aldolase B Deficiency .
Fructose Intolerances .
Fructose Intolerances, Hereditary .
Fructose-1,6-Biphosphate Aldolase Deficiencies .
Fructose-1-Phosphate Aldolase Deficiencies .
Fructosemias .
Hereditary Fructose Intolerances .
Intolerance, Fructose .
Intolerances, Fructose .
An autosomal recessive fructose metabolism disorder due to deficient fructose-1-phosphate aldolase (EC 2.1.2.13) activity, resulting in accumulation of fructose-1-phosphate. The accumulated fructose-1-phosphate inhibits glycogenolysis and gluconeogenesis, causing severe hypoglycemia following ingestion of fructose. Prolonged fructose ingestion in infants leads ultimately to hepatic failure and death. Patients develop a strong distaste for sweet food, and avoid a chronic course of the disease by remaining on a fructose- and sucrose-free diet. .
0.88
8349
 
Fructosamine .
D-Isoglucosamine .
D Isoglucosamine .
An amino sugar formed when glucose non-enzymatically reacts with the N-terminal amino group of proteins. The fructose moiety is derived from glucose by the "classical" Amadori rearrangement. .
0.79
141429
 
Fructosephosphates .
0.74
21667
 
Fructans .
Levans .
Polysaccharides composed of D-fructose units. .
0.74
23865
 
Fructosediphosphates .
Diphosphoric acid esters of fructose. The fructose-1,6- diphosphate isomer is most prevalent. It is an important intermediate in the glycolysis process. .
0.71
61690
 
Fructose-Bisphosphatase .
D-Fructose-1,6-Bisphosphate 1-Phosphohydrolase .
FDPase .
Fructose-1,6-Biphosphatase .
1-Phosphohydrolase, D-Fructose-1,6-Bisphosphate .
D Fructose 1,6 Bisphosphate 1 Phosphohydrolase .
Fructose 1,6 Biphosphatase .
Fructose 1,6 Bisphosphatase .
Fructose 1,6 Diphosphatase .
Fructose Bisphosphatase .
Fructose-1,6-Bisphosphatase .
Fructosediphosphatase .
Hexosediphosphatase .
Fructose-1,6-Diphosphatase .
An enzyme that catalyzes the conversion of D-fructose 1,6-bisphosphate and water to D-fructose 6-phosphate and orthophosphate. EC 3.1.3.11. .
0.69
122184