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 DeCS Categories

C10 Nervous System Diseases .
C10.228 Central Nervous System Diseases .
C10.228.140 Brain Diseases .
C10.228.140.163 Brain Diseases, Metabolic .
C10.228.140.163.100 Brain Diseases, Metabolic, Inborn .
C10.228.140.163.100.362 Hereditary Central Nervous System Demyelinating Diseases .
C10.228.140.163.100.362.500 Leukodystrophy, Globoid Cell .
C10.228.140.163.100.362.550 Leukodystrophy, Metachromatic .
C10.228.140.163.100.435 Lysosomal Storage Diseases, Nervous System .
C10.228.140.163.100.435.825 Sphingolipidoses .
C10.228.140.163.100.435.825.590 Leukodystrophy, Globoid Cell .
C10.228.140.163.100.435.825.850 Sulfatidosis .
C10.228.140.163.100.435.825.850.500 Leukodystrophy, Metachromatic .
C10.228.140.695 Leukoencephalopathies .
C10.228.140.695.625 Hereditary Central Nervous System Demyelinating Diseases .
C10.228.140.695.625.500 Leukodystrophy, Globoid Cell .
C10.228.140.695.625.550 Leukodystrophy, Metachromatic .
C10.314 Demyelinating Diseases .
C10.314.400 Hereditary Central Nervous System Demyelinating Diseases .
C10.314.400.500 Leukodystrophy, Globoid Cell .
C10.314.400.550 Leukodystrophy, Metachromatic .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.565 Metabolism, Inborn Errors .
C16.320.565.189 Brain Diseases, Metabolic, Inborn .
C16.320.565.189.362 Hereditary Central Nervous System Demyelinating Diseases .
C16.320.565.189.362.500 Leukodystrophy, Globoid Cell .
C16.320.565.189.362.550 Leukodystrophy, Metachromatic .
C16.320.565.189.435 Lysosomal Storage Diseases, Nervous System .
C16.320.565.189.435.825 Sphingolipidoses .
C16.320.565.189.435.825.590 Leukodystrophy, Globoid Cell .
C16.320.565.189.435.825.850 Sulfatidosis .
C16.320.565.189.435.825.850.500 Leukodystrophy, Metachromatic .
C16.320.565.398 Lipid Metabolism, Inborn Errors .
C16.320.565.398.641 Lipidoses .
C16.320.565.398.641.803 Sphingolipidoses .
C16.320.565.398.641.803.585 Leukodystrophy, Globoid Cell .
C16.320.565.398.641.803.925 Sulfatidosis .
C16.320.565.398.641.803.925.500 Leukodystrophy, Metachromatic .
C16.320.565.595 Lysosomal Storage Diseases .
C16.320.565.595.554 Lysosomal Storage Diseases, Nervous System .
C16.320.565.595.554.825 Sphingolipidoses .
C16.320.565.595.554.825.590 Leukodystrophy, Globoid Cell .
C16.320.565.595.554.825.850 Sulfatidosis .
C16.320.565.595.554.825.850.500 Leukodystrophy, Metachromatic .
C18 Nutritional and Metabolic Diseases .
C18.452 Metabolic Diseases .
C18.452.132 Brain Diseases, Metabolic .
C18.452.132.100 Brain Diseases, Metabolic, Inborn .
C18.452.132.100.362 Hereditary Central Nervous System Demyelinating Diseases .
C18.452.132.100.362.500 Leukodystrophy, Globoid Cell .
C18.452.132.100.362.550 Leukodystrophy, Metachromatic .
C18.452.132.100.435 Lysosomal Storage Diseases, Nervous System .
C18.452.132.100.435.825 Sphingolipidoses .
C18.452.132.100.435.825.590 Leukodystrophy, Globoid Cell .
C18.452.132.100.435.825.850 Sulfatidosis .
C18.452.132.100.435.825.850.500 Leukodystrophy, Metachromatic .
C18.452.584 Lipid Metabolism Disorders .
C18.452.584.500 Dyslipidemias .
C18.452.584.500.500 Hyperlipidemias .
C18.452.584.687 Lipidoses .
C18.452.584.687.803 Sphingolipidoses .
C18.452.584.687.803.585 Leukodystrophy, Globoid Cell .
C18.452.584.687.803.925 Sulfatidosis .
C18.452.584.687.803.925.500 Leukodystrophy, Metachromatic .
C18.452.648 Metabolism, Inborn Errors .
C18.452.648.189 Brain Diseases, Metabolic, Inborn .
C18.452.648.189.362 Hereditary Central Nervous System Demyelinating Diseases .
C18.452.648.189.362.500 Leukodystrophy, Globoid Cell .
C18.452.648.189.362.550 Leukodystrophy, Metachromatic .
C18.452.648.189.435 Lysosomal Storage Diseases, Nervous System .
C18.452.648.189.435.825 Sphingolipidoses .
C18.452.648.189.435.825.590 Leukodystrophy, Globoid Cell .
C18.452.648.189.435.825.850 Sulfatidosis .
C18.452.648.189.435.825.850.500 Leukodystrophy, Metachromatic .
C18.452.648.398 Lipid Metabolism, Inborn Errors .
C18.452.648.398.641 Lipidoses .
C18.452.648.398.641.803 Sphingolipidoses .
C18.452.648.398.641.803.585 Leukodystrophy, Globoid Cell .
C18.452.648.398.641.803.925 Sulfatidosis .
C18.452.648.398.641.803.925.500 Leukodystrophy, Metachromatic .
C18.452.648.595 Lysosomal Storage Diseases .
C18.452.648.595.554 Lysosomal Storage Diseases, Nervous System .
C18.452.648.595.554.825 Sphingolipidoses .
C18.452.648.595.554.825.590 Leukodystrophy, Globoid Cell .
C18.452.648.595.554.825.850 Sulfatidosis .
C18.452.648.595.554.825.850.500 Leukodystrophy, Metachromatic .
D02 Organic Chemicals .
D02.241 Carboxylic Acids .
D02.241.081 Acids, Acyclic .
D02.241.081.114 Butyrates .
D02.241.081.114.968 Isobutyrates .
D02.241.081.114.968.500 Fibric Acids .
D02.241.081.114.968.500.625 Fenofibrate .
D02.355 Ethers .
D02.355.726 Phenyl Ethers .
D02.355.726.305 Fibric Acids .
D02.355.726.305.625 Fenofibrate .
D02.455 Hydrocarbons .
D02.455.426 Hydrocarbons, Cyclic .
D02.455.426.559 Hydrocarbons, Aromatic .
D02.455.426.559.389 Benzene Derivatives .
D02.455.426.559.389.134 Benzophenones .
D02.455.426.559.389.134.750 Fenofibrate .
D02.455.426.559.389.657 Phenols .
D02.455.426.559.389.657.654 Phenyl Ethers .
D02.455.426.559.389.657.654.305 Fibric Acids .
D02.455.426.559.389.657.654.305.625 Fenofibrate .
D02.522 Ketones .
D02.522.223 Benzophenones .
D02.522.223.750 Fenofibrate .
D09 Carbohydrates .
D09.698 Polysaccharides .
D09.698.718 Polysaccharides, Bacterial .
D09.698.718.450 Lipopolysaccharides .
D09.698.718.450.500 Lipid A .
D10 Lipids .
D10.494 Lipopolysaccharides .
D10.494.500 Lipid A .
D23 Biological Factors .
D23.050 Antigens .
D23.050.161 Antigens, Bacterial .
D23.050.161.616 Polysaccharides, Bacterial .
D23.050.161.616.525 Lipopolysaccharides .
D23.050.161.616.525.500 Lipid A .
D23.946 Toxins, Biological .
D23.946.123 Bacterial Toxins .
D23.946.123.329 Endotoxins .
D23.946.123.329.500 Lipopolysaccharides .
D23.946.123.329.500.500 Lipid A .
 
 Terms
 Synonyms & Historicals
Documents
LILACS e MDL
 
Lipidoses .
Lipoidosis .
Lipidosis .
Lipoidoses .
Conditions characterized by abnormal lipid deposition due to disturbance in lipid metabolism, such as hereditary diseases involving lysosomal enzymes required for lipid breakdown. They are classified either by the enzyme defect or by the type of lipid involved. .
1.00
182576
 
Lipids .
Lipids and Antilipemic Agents .
A generic term for fats and lipoids, the alcohol-ether-soluble constituents of protoplasm, which are insoluble in water. They comprise the fats, fatty oils, essential oils, waxes, phospholipids, glycolipids, sulfolipids, aminolipids, chromolipids (lipochromes), and fatty acids. (Grant & Hackh's Chemical Dictionary, 5th ed) .
0.75
142894231
 
Leukodystrophy, Globoid Cell .
Classic Globoid Cell Leukodystrophy .
Early-Onset Globoid Cell Leukodystrophy .
GALC Deficiency .
Galactocerebrosidase Deficiency .
Galactosylceramide Lipidosis .
Galactosylceramide beta-Galactosidase Deficiency .
Galactosylceramide-beta-Galactosidase Deficiency Disease .
Galactosylcerebrosidase Deficiency .
Galactosylsphingosine Lipidosis .
Globoid Body Sclerosis, Diffuse .
Globoid Cell Leukodystrophy .
Globoid Cell Leukoencephalopathy .
Globoid Leukodystrophy .
Infantile Globoid Cell Leukodystrophy .
Krabbe Leukodystrophy .
Krabbe's Disease .
Krabbe's Leukodystrophy .
Late-Onset Globoid Cell Leukodystrophy .
Leukodystrophy, Globoid Cell, Classic .
Leukodystrophy, Globoid Cell, Early-Onset .
Leukodystrophy, Globoid Cell, Infantile .
Leukodystrophy, Globoid Cell, Late-Onset .
Psychosine Lipidosis .
Cell Leukodystrophies, Globoid .
Cell Leukodystrophy, Globoid .
Cell Leukoencephalopathies, Globoid .
Cell Leukoencephalopathy, Globoid .
Deficiencies, GALC .
Deficiencies, Galactocerebrosidase .
Deficiencies, Galactosylceramide beta-Galactosidase .
Deficiency Disease, Galactosylceramidase .
Deficiency Disease, Galactosylceramide-beta-Galactosidase .
Deficiency Diseases, Galactosylceramidase .
Deficiency Diseases, Galactosylceramide-beta-Galactosidase .
Deficiency, GALC .
Deficiency, Galactocerebrosidase .
Deficiency, Galactosylceramide beta-Galactosidase .
Disease, Galactosylceramidase Deficiency .
Disease, Galactosylceramide-beta-Galactosidase Deficiency .
Diseases, Galactosylceramidase Deficiency .
Diseases, Galactosylceramide-beta-Galactosidase Deficiency .
Early Onset Globoid Cell Leukodystrophy .
GALC Deficiencies .
Galactocerebrosidase Deficiencies .
Galactosylceramidase Deficiency Diseases .
Galactosylceramide beta Galactosidase Deficiency .
Galactosylceramide beta Galactosidase Deficiency Disease .
Galactosylceramide beta-Galactosidase Deficiencies .
Galactosylceramide-beta-Galactosidase Deficiency Diseases .
Globoid Cell Leukodystrophies .
Globoid Cell Leukoencephalopathies .
Globoid Leukodystrophies .
Krabbes Disease .
Krabbes Leukodystrophy .
Late Onset Globoid Cell Leukodystrophy .
Leukodystrophies, Globoid .
Leukodystrophies, Globoid Cell .
Leukodystrophy, Globoid .
Leukodystrophy, Krabbe .
Leukodystrophy, Krabbe's .
Leukoencephalopathies, Globoid Cell .
Leukoencephalopathy, Globoid Cell .
beta-Galactosidase Deficiencies, Galactosylceramide .
beta-Galactosidase Deficiency, Galactosylceramide .
Krabbe Disease .
Diffuse Globoid Body Sclerosis .
Galactosylceramidase Deficiency Disease .
An autosomal recessive metabolic disorder caused by a deficiency of GALACTOSYLCERAMIDASE leading to intralysosomal accumulation of galactolipids such as GALACTOSYLCERAMIDES and PSYCHOSINE. It is characterized by demyelination associated with large multinucleated globoid cells, predominantly involving the white matter of the central nervous system. The loss of MYELIN disrupts normal conduction of nerve impulses. .
0.71
12895
 
Leukodystrophy, Metachromatic .
ARSA Deficiency .
Arylsulfatase A Deficiency .
Cerebral sclerosis, Diffuse, Metachromatic Form .
Cerebroside Sulfatase Deficiency .
Greenfield Disease .
Greenfield's Disease .
Leukodystrophy, Metachromatic, Adult .
Leukodystrophy, Metachromatic, Juvenile .
Metachromatic Leukodystrophy .
Metachromatic Leukodystrophy, Adult .
Metachromatic Leukodystrophy, Adult-Type .
Metachromatic Leukodystrophy, Infant .
Metachromatic Leukodystrophy, Infant-Type .
Metachromatic Leukodystrophy, Juvenile .
Metachromatic Leukodystrophy, Juvenile-Type .
Metachromatic Leukodystrophy, Late Infantile .
Metachromatic Leukoencephalopathy .
Sulfatide Lipidosis .
ARSA Deficiencies .
Adult Metachromatic Leukodystrophies .
Adult Metachromatic Leukodystrophy .
Adult-Type Metachromatic Leukodystrophies .
Adult-Type Metachromatic Leukodystrophy .
Arylsulfatase A Deficiencies .
Cerebroside Sulfatase Deficiencies .
Deficiencies, ARSA .
Deficiencies, Arylsulfatase A .
Deficiencies, Cerebroside Sulfatase .
Deficiency, ARSA .
Deficiency, Arylsulfatase A .
Deficiency, Cerebroside Sulfatase .
Infant Metachromatic Leukodystrophies .
Infant Metachromatic Leukodystrophy .
Infant-Type Metachromatic Leukodystrophies .
Infant-Type Metachromatic Leukodystrophy .
Juvenile Metachromatic Leukodystrophies .
Juvenile Metachromatic Leukodystrophy .
Juvenile-Type Metachromatic Leukodystrophies .
Juvenile-Type Metachromatic Leukodystrophy .
Leukodystrophies, Adult Metachromatic .
Leukodystrophies, Adult-Type Metachromatic .
Leukodystrophies, Juvenile Metachromatic .
Leukodystrophies, Juvenile-Type Metachromatic .
Leukodystrophies, Metachromatic .
Leukodystrophy, Adult Metachromatic .
Leukodystrophy, Adult-Type Metachromatic .
Leukodystrophy, Juvenile Metachromatic .
Leukodystrophy, Juvenile-Type Metachromatic .
Leukoencephalopathies, Metachromatic .
Leukoencephalopathy, Metachromatic .
Lipidosis, Sulfatide .
Metachromatic Leukodystrophies .
Metachromatic Leukodystrophies, Adult .
Metachromatic Leukodystrophies, Adult-Type .
Metachromatic Leukodystrophies, Infant .
Metachromatic Leukodystrophies, Infant-Type .
Metachromatic Leukodystrophies, Juvenile .
Metachromatic Leukodystrophies, Juvenile-Type .
Metachromatic Leukodystrophy, Adult Type .
Metachromatic Leukodystrophy, Infant Type .
Metachromatic Leukodystrophy, Juvenile Type .
Metachromatic Leukoencephalopathies .
Sulfatase Deficiencies, Cerebroside .
Sulfatase Deficiency, Cerebroside .
Arylsulfatase A Deficiency Disease .
Cerebroside Sulphatase Deficiency Disease .
An autosomal recessive metabolic disease caused by a deficiency of CEREBROSIDE-SULFATASE leading to intralysosomal accumulation of cerebroside sulfate (SULFOGLYCOSPHINGOLIPIDS) in the nervous system and other organs. Pathological features include diffuse demyelination, and metachromatically-staining granules in many cell types such as the GLIAL CELLS. There are several allelic and nonallelic forms with a variety of neurological symptoms. .
0.70
161123
 
Fenofibrate .
Antara Micronized Procetofen .
Apo-Feno-Micro .
Apo-Fenofibrate .
CiL 8694 .
Controlip .
Fenobeta .
Fenofanton .
Fenofibrat AL .
Fenofibrat AZU .
Fenofibrat AbZ .
Fenofibrat FPh .
Fenofibrat Heumann .
Fenofibrat Hexal .
Fenofibrat Stada .
Fenofibrat-ratiopharm .
Fénofibrate Debat .
Fénofibrate MSD .
Gen-Fenofibrate .
LF-178 .
Lipanthyl .
Lipantil .
Liparison .
Lipidil .
Lipidil-Ter .
Livesan .
Lofibra .
MTW-Fenofibrat .
Normalip .
Novo-Fenofibrate .
Nu-Fenofibrate .
PMS-Fenofibrate Micro .
Phenofibrate .
Procetofene .
Secalip .
Supralip .
Tricor .
durafenat .
fenofibrat von ct .
AZU, Fenofibrat .
Apo Feno Micro .
Apo Fenofibrate .
Debat, Fénofibrate .
Fenofibrat ratiopharm .
Gen Fenofibrate .
Heumann, Fenofibrat .
Hexal, Fenofibrat .
LF 178 .
LF178 .
Lipidil Ter .
MTW Fenofibrat .
Micronized Procetofen, Antara .
Novo Fenofibrate .
Nu Fenofibrate .
PMS Fenofibrate Micro .
Procetofen, Antara Micronized .
Stada, Fenofibrat .
Procetofen .
LIPANTHYL .
An antilipemic agent which reduces both CHOLESTEROL and TRIGLYCERIDES in the blood. .
0.69
92393
 
Lipid A .
Lipid A is the biologically active component of lipopolysaccharides. It shows strong endotoxic activity and exhibits immunogenic properties. .
0.66
33424
 
Hyperlipidemias .
Hyperlipidemia .
Lipemia .
Lipidemia .
Hyperlipemias .
Lipemias .
Lipidemias .
Hyperlipemia .
Conditions with excess LIPIDS in the blood. .
0.65
70124372