DeCS Categories
C15 Hemic and Lymphatic Diseases .
C15.378 Hematologic Diseases .
C15.378.071 Anemia .
C15.378.071.141 Anemia, Hemolytic .
C15.378.071.141.125 Anemia, Hemolytic, Autoimmune .
C15.378.071.141.150 Anemia, Hemolytic, Congenital .
C15.378.100 Blood Coagulation Disorders .
C15.378.100.802 Purpura .
C15.378.100.802.687 Purpura, Thrombocytopenic .
C15.378.100.802.687.680 Purpura, Thrombotic Thrombocytopenic .
C15.378.140 Blood Platelet Disorders .
C15.378.140.855 Thrombocytopenia .
C15.378.140.855.925 Thrombotic Microangiopathies .
C15.378.140.855.925.750 Purpura, Thrombocytopenic .
C15.378.140.855.925.750.680 Purpura, Thrombotic Thrombocytopenic .
C15.378.925 Thrombophilia .
C15.378.925.850 Purpura, Thrombotic Thrombocytopenic .
C16 Congenital, Hereditary, and Neonatal Diseases and Abnormalities .
C16.320 Genetic Diseases, Inborn .
C16.320.070 Anemia, Hemolytic, Congenital .
C20 Immune System Diseases .
C20.111 Autoimmune Diseases .
C20.111.175 Anemia, Hemolytic, Autoimmune .
C23 Pathological Conditions, Signs and Symptoms .
C23.550 Pathologic Processes .
C23.550.414 Hemorrhage .
C23.550.414.950 Purpura .
C23.550.414.950.687 Purpura, Thrombocytopenic .
C23.550.414.950.687.680 Purpura, Thrombotic Thrombocytopenic .
C23.888 Signs and Symptoms .
C23.888.885 Skin Manifestations .
C23.888.885.687 Purpura .
C23.888.885.687.687 Purpura, Thrombocytopenic .
C23.888.885.687.687.680 Purpura, Thrombotic Thrombocytopenic .
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| | Terms Synonyms & Historicals | Documents LILACS e MDL | | | | |
| Purpura, Thrombotic Thrombocytopenic . Congenital Thrombotic Thrombocytopenic Purpura . Familial Thrombotic Thrombocytopenia Purpura . Familial Thrombotic Thrombocytopenic Purpura . Microangiopathic Hemolytic Anemia, Congenital . Moschcowitz Disease . Schulman-Upshaw Syndrome . Thrombotic Microangiopathy, Familial . Thrombotic Thrombocytopenic Purpura . Upshaw Factor, Deficiency of . Upshaw-Schulman Syndrome . Disease, Moschcowitz . Disease, Moschkowitz . Familial Thrombotic Microangiopathy . Microangiopathy, Familial Thrombotic . Schulman Upshaw Syndrome . Syndrome, Schulman-Upshaw . Syndrome, Upshaw-Schulman . Thrombocytopenic Purpura, Thrombotic . Thrombopenic Purpura, Thrombotic . Thrombotic Thrombopenic Purpura . Upshaw Schulman Syndrome . Purpura, Thrombotic Thrombopenic . Moschkowitz Disease . Thrombotic Thrombocytopenic Purpura, Congenital . Thrombotic Thrombocytopenic Purpura, Familial . An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. . 0.89
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| Anemia, Hemolytic, Autoimmune . Acquired Autoimmune Hemolytic Anemia . Anemia, Hemolytic, Cold Antibody . Cold Antibody Disease . Cold Antibody Hemolytic Anemia . Idiopathic Autoimmune Hemolytic Anemia . Agglutinin Disease, Cold . Agglutinin Diseases, Cold . Anemia, Autoimmune Hemolytic . Anemias, Autoimmune Hemolytic . Autoimmune Hemolytic Anemias . Cold Agglutinin Diseases . Cold Antibody Diseases . Disease, Cold Agglutinin . Disease, Cold Antibody . Diseases, Cold Agglutinin . Diseases, Cold Antibody . Hemolytic Anemias, Autoimmune . Anemia, Hemolytic, Idiopathic Acquired . Autoimmune Hemolytic Anemia . Cold Agglutinin Disease . Hemolytic Anemia, Autoimmune . Acquired hemolytic anemia due to the presence of AUTOANTIBODIES which agglutinate or lyse the patient's own RED BLOOD CELLS. . 0.59
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| Anemia, Hemolytic, Congenital . Congenital Hemolytic Anemia . Hemolytic Anemia, Congenital . Hemolytic Anemia, Hereditary . Hereditary Hemolytic Anemia . Anemia, Congenital Hemolytic . Anemia, Hereditary Hemolytic . Anemias, Congenital Hemolytic . Anemias, Hereditary Hemolytic . Congenital Hemolytic Anemias . Hemolytic Anemias, Congenital . Hemolytic Anemias, Hereditary . Hereditary Hemolytic Anemias . Anemia, Hemolytic, Hereditary . Hemolytic anemia due to various intrinsic defects of the erythrocyte. . 0.58
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