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alpha Ketoisovalerate Dehydrogenase CID10 - Classificação Internacional de Doenças DeCS Português DeCS Inglês DeCS Espanhol DeCS Espanha DeCS Português com escopo DeCS Inglês com escopo DeCS Espanhol com escopo DeCS Espanha com escopo LILACS - LILACS Regional
DeCS Categories D05 Macromolecular Substances . D05.500 Multiprotein Complexes . D05.500.562 Multienzyme Complexes . D05.500.562.468 Ketoglutarate Dehydrogenase Complex . D08 Enzymes and Coenzymes . D08.811 Enzymes . D08.811.600 Multienzyme Complexes . D08.811.600.465 Ketoglutarate Dehydrogenase Complex . D08.811.682 Oxidoreductases . D08.811.682.657 Oxidoreductases Acting on Aldehyde or Oxo Group Donors . D08.811.682.657.350 Ketone Oxidoreductases . D08.811.682.657.350.750 Ketoglutarate Dehydrogenase Complex . D08.811.682.657.350.760 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) . D08.811.682.657.350.825 2-Oxoisovalerate Dehydrogenase (Acylating) .		Terms  Synonyms & Historicals Documents LILACS e MDL   2-Oxoisovalerate Dehydrogenase (Acylating) . 2-Oxoisovalerate Dehydrogenase . alpha-Ketoisovalerate Dehydrogenase . 2 Oxoisovalerate Dehydrogenase . Dehydrogenase, 2-Oxoisovalerate . Dehydrogenase, alpha-Ketoisovalerate . alpha Ketoisovalerate Dehydrogenase . An NAD+ dependent enzyme that catalyzes the oxidation 3-methyl-2-oxobutanoate to 2-methylpropanoyl-CoA. It plays a role in the degradation of VALINE; LEUCINE; and ISOLEUCINE. . 1.00 0 6   Ketoglutarate Dehydrogenase Complex . 2-Keto-4-Hydroxyglutarate Dehydrogenase . 2-Oxoglutarate Dehydrogenase . 2-Oxoglutarate Dehydrogenase Complex . Oxoglutarate Dehydrogenase . alpha-Ketoglutarate Dehydrogenase . alpha-Ketoglutarate Dehydrogenase Complex . 2 Keto 4 Hydroxyglutarate Dehydrogenase . 2 Oxoglutarate Dehydrogenase . 2 Oxoglutarate Dehydrogenase Complex . Complex, 2-Oxoglutarate Dehydrogenase . Complex, Ketoglutarate Dehydrogenase . Complex, alpha-Ketoglutarate Dehydrogenase . Dehydrogenase Complex, 2-Oxoglutarate . Dehydrogenase Complex, Ketoglutarate . Dehydrogenase Complex, alpha-Ketoglutarate . Dehydrogenase, 2-Keto-4-Hydroxyglutarate . Dehydrogenase, 2-Oxoglutarate . Dehydrogenase, Oxoglutarate . Dehydrogenase, alpha-Ketoglutarate . alpha Ketoglutarate Dehydrogenase . alpha Ketoglutarate Dehydrogenase Complex . 0.77 0 990   3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) . 2-Oxoisocaproate Dehydrogenase . Alpha-Keto Acid Dehydrogenase . BCKA Decarboxylase . Branched Chain Alpha-Keto Acid Decarboxylase . Branched Chain Ketoacid Dehydrogenase . Branched-Chain 2-Oxo Acid Dehydrogenase . Branched-Chain Keto Acid Dehydrogenase . Branched-Chain Oxo-Acid Dehydrogenase . 2 Oxoisocaproate Dehydrogenase . Acid Dehydrogenase, Alpha-Keto . Alpha Keto Acid Dehydrogenase . Branched Chain 2 Oxo Acid Dehydrogenase . Branched Chain Alpha Keto Acid Decarboxylase . Branched Chain Keto Acid Dehydrogenase . Branched Chain Oxo Acid Dehydrogenase . Decarboxylase, BCKA . Dehydrogenase, 2-Oxoisocaproate . Dehydrogenase, Alpha-Keto Acid . Dehydrogenase, Branched-Chain Oxo-Acid . Oxo-Acid Dehydrogenase, Branched-Chain . 2-Oxoisovalerate Dehydrogenase (Lipoamide) . A ketone oxidoreductase that catalyzes the overall conversion of alpha-keto acids to ACYL-CoA and CO2. The enzyme requires THIAMINE DIPHOSPHATE as a cofactor. Defects in genes that code for subunits of the enzyme are a cause of MAPLE SYRUP URINE DISEASE. The enzyme was formerly classified as EC 1.2.4.3. . 0.74 0 694